1 by Wardah R.I 21/03/2014 Disorder of vestibular system dr. Wardah Rahmatul Islamiyah, SpS
1 by Wardah RI 21032014
Disorder of
vestibular system
dr Wardah Rahmatul Islamiyah SpS
2 by Wardah RI 21032014
DESKRIPSI
1 Merupakan suatu sensasi perub orientasi thd ruang
2 Dpt disebabkan oleh bbrp mekanisme patofisiologi yg berbeda2
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ANAMNESIS
1 Deskripsi sensasi
2 Bagaimana mulainya
3 Berapa lama
4 Berapa sering terjadi
5 Faktor yang mencetuskan
6 Gejala2 yg menyertai
7 Terapi
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EPIDEMIOLOGI DIZZINESS
bull Lazim pd semua kelompok
bull gt wanita
bull Prevalensi meningkat seiring bertambahnya usia
bull Presyncope dan vertigo merupakan subtipe yg paling lazim (13 px dg keluhan dizziness)
Evaluation of the lsquoDizzyrsquo patient
Nasher
Posture is controlled by two basic mechanisms
1 Local regulation from spinal reflexes commanded by information from muscle and tendon stretch receptors
2 Regulation from extra spinal feedback such as input from the vestibular system
3 Visual input
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
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KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
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PRESYNCOPE
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PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
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PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
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DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
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TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
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TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
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TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
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PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
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PSIKOFISIOLOGIS
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PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
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TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
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PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
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DISEQUILIBRIUM
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PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
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TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
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PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
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VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
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PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
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bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
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CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
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OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
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REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
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SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
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BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
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bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
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50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
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DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
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bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
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MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
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BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
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INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
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PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
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PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
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Vestibulopathy perifer acute = neuritis vestibular
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PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
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DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
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TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
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VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
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PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
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PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
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KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
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DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
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bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
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PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
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PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
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AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
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Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
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Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
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Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
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Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
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Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
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CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
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DESKRIPSI
1 Merupakan suatu sensasi perub orientasi thd ruang
2 Dpt disebabkan oleh bbrp mekanisme patofisiologi yg berbeda2
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ANAMNESIS
1 Deskripsi sensasi
2 Bagaimana mulainya
3 Berapa lama
4 Berapa sering terjadi
5 Faktor yang mencetuskan
6 Gejala2 yg menyertai
7 Terapi
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EPIDEMIOLOGI DIZZINESS
bull Lazim pd semua kelompok
bull gt wanita
bull Prevalensi meningkat seiring bertambahnya usia
bull Presyncope dan vertigo merupakan subtipe yg paling lazim (13 px dg keluhan dizziness)
Evaluation of the lsquoDizzyrsquo patient
Nasher
Posture is controlled by two basic mechanisms
1 Local regulation from spinal reflexes commanded by information from muscle and tendon stretch receptors
2 Regulation from extra spinal feedback such as input from the vestibular system
3 Visual input
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
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KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
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PRESYNCOPE
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PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
3 by Wardah RI 21032014
ANAMNESIS
1 Deskripsi sensasi
2 Bagaimana mulainya
3 Berapa lama
4 Berapa sering terjadi
5 Faktor yang mencetuskan
6 Gejala2 yg menyertai
7 Terapi
4 by Wardah RI 21032014
EPIDEMIOLOGI DIZZINESS
bull Lazim pd semua kelompok
bull gt wanita
bull Prevalensi meningkat seiring bertambahnya usia
bull Presyncope dan vertigo merupakan subtipe yg paling lazim (13 px dg keluhan dizziness)
Evaluation of the lsquoDizzyrsquo patient
Nasher
Posture is controlled by two basic mechanisms
1 Local regulation from spinal reflexes commanded by information from muscle and tendon stretch receptors
2 Regulation from extra spinal feedback such as input from the vestibular system
3 Visual input
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
4 by Wardah RI 21032014
EPIDEMIOLOGI DIZZINESS
bull Lazim pd semua kelompok
bull gt wanita
bull Prevalensi meningkat seiring bertambahnya usia
bull Presyncope dan vertigo merupakan subtipe yg paling lazim (13 px dg keluhan dizziness)
Evaluation of the lsquoDizzyrsquo patient
Nasher
Posture is controlled by two basic mechanisms
1 Local regulation from spinal reflexes commanded by information from muscle and tendon stretch receptors
2 Regulation from extra spinal feedback such as input from the vestibular system
3 Visual input
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Evaluation of the lsquoDizzyrsquo patient
Nasher
Posture is controlled by two basic mechanisms
1 Local regulation from spinal reflexes commanded by information from muscle and tendon stretch receptors
2 Regulation from extra spinal feedback such as input from the vestibular system
3 Visual input
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
9
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
10
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Evaluation of the lsquoDizzyrsquo patient
II Which Converging System Is Involved
A Oculomotor (Visual)
B Proprioceptive
C Vestibular
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
16 by Wardah RI 21032014
KLASIFIKASI (SUBTIPE TERSERING)
1 Fisiologis = mabuk gerakan
2 PRESYNCOPE (near-faint) 4-14
Kepala teras ringan sensasi sebelum hilangnya kesadaran atau jatuh
3 PSIKOFISIOLOGIS 2 ndash 16
Disosiasi ldquomengambangrdquo ldquoberenangrdquo
4 DISEQUILIBRIUM 2
ldquoDizzyrdquo tdk seimbang yg timbul hanya ketika berdiri atau berjalan tdk berhub dg sensasi kepala yg abnormal
5 VERTIGO 50
Ilusi gerakan rotasi kdg px merasa perpindahan linier atau diangkat
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
17 by Wardah RI 21032014
PRESYNCOPE
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
18 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull Berlt CBF
bull Light headedness
bull Jika CBF ltltlt rarr syncope
bull ARITMIA bull episode syncope berulang
bull terjadi pd berbagai posisi
bull Disertai keluhan cardiac lainnya (nyeri dada atau palpitasi)
bull HIPOTENSI ORTOSTATIK bull Blood loss akut
bull Volume lt
bull Tx diuretik atau anti hipertensi
bull Ketika px berdiri drh terkumpul di tungkai dan vaskuler splanchnic (gravitasi)
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
19 by Wardah RI 21032014
PATOFISIOLOGI - PRESYNCOPE
bull VASOVAGAL
bull Presyncope yg diperantarai neural
bull Terjadi ketika pasien berdiri
bull TD tdk menurun sesaat ketika px berdiri
bull Mx
bull Signal aferen dr mekanoreseptor arterial viseral
bull HIPERVENTILASI
bull Menurunnya kadar CO2 dlm drh
bull Konstriksi pemb darah cerebral
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
20 by Wardah RI 21032014
DIAGNOSIS - PRESYNCOPE
a Hipotensi ortostatik pedarr TD gt 10 ndash 15 mmHg ketika pasien berubah posisi dari berbaring ke berdiri
b Aritmia cardiac
Pasien presyncope episodic
ECG sinus pauses sinus bradikardi atrial fibrilasi dan supraventricular takikardi
c Vasodepressor presyncope anamnesis khas pd px tanpa ggn neurologis atau cardiovaskuler
d Hiperventilasi gx khas yg menyertai rarr
anxiety dyspnea
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
21 by Wardah RI 21032014
TERAPI - PRESYNCOPE
1 HIPOTENSI ORTOSTATIK
bull Hentikan obat2an atau koreksi faktor2 yg menyebabkan penurunan volume darah
bull Px dg insufisiensi otonom berikan intake tinggi garam utk meningkatkan volume darah dan menggunakan elastic stocking utk mencegah pengumpulan darah pada ekstremitas inferior
bull Pd kasus berat
bull Steroid fluocortisone (yg dpt menahan garam) menambah volume darah
bull 1 adrenergik agonis (midodrine) meningkatkan tonus vaskuler
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
22 by Wardah RI 21032014
TERAPI - PRESYNCOPE
2 VASOVAGAL PRESYNCOPE
bull KIE mengenai perjlnan dan mekanisme penyakit
bull Pemberian intake tinggi garam dan cairan
bull Hindari kondisi yg dpt menjadi predisposisi terjadinya hipotensi atau dehidrasi
bull Penggunaan obat beta blocker midodrine serotonin reuptake inhibitor ACE inhibitor fluorocortisone (tp hsl RCT efek = plasebo)
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
23 by Wardah RI 21032014
TERAPI - PRESYNCOPE
3 PENYAKIT JTG bull Ggn cardiac output merupakan warning sign dan
resiko kematian mendadak
bull Penatalaksanaan aritmia tgt perjalanan penyakit yg mendasari atau pemasangan pacemaker
4 HIPERVENTILASI bull KIE
bull Fisioterapi dan psikoterapi
bull Tx farmakologis
bull Tricyclic amine
bull Selective serotonine reuptake inhibitor rarr panic disorder
bull Tranquilizer jangka panjang dihindari karena efek ketergantungan
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
24 by Wardah RI 21032014
PROGNOSIS
bull Benign
bull Masalah jtg mengancam jiwa
bull Hipotensi ortostatik berkaitan dg penyakit2 neurologis degeneratif (Shy-Drager dan Parkinson) rarr
disabilitas berat
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
25 by Wardah RI 21032014
PSIKOFISIOLOGIS
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
26 by Wardah RI 21032014
PATOFISIOLOGI - PSIKOFISIOLOGIS bull Mx
bull Akibat gangguan integrasi central dari signal sensoris
bull Sering disertai anxietas akut atau kronis
DIAGNOSIS - PSIKOFISIOLOGIS
a Disertai gejala anxietas akut dan kronis
b Pasien terfokus pada gx somatik dizziness dan gx otonom
Intensitas lebih berat dp intensitas anxietas
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
27 by Wardah RI 21032014
TERAPI - PSIKOFISIOLOGI
bull KIE bahwa gx yg ditimbulkan benar2 akibat perub fisiologis
bull Tiga kelompok obat yg lazim digunakan pd kasus panic disorder (penggunaan alprazolam bisa menyebabkan ketergantungan shg hati2)
1 Tricyclic amine (imipramine amp desipramine)
2 Benzodiazemine potensi tinggi (alprazolam)
3 SSRI (paroxetine dan fluoxetine)
bull Tx suportif psikoterapi (behavioral tx)
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
28 by Wardah RI 21032014
PROGNOSIS
bull Bertahan selama bbrp thn
bull Kambuh setelah periode remisi yg panjang
bull Keluhan sepanjang hari
bull Intensitas bervariasi sesuai tingkat stress
bull Berhub dg keluhan panik dan fobia (agorafobia)
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
29 by Wardah RI 21032014
DISEQUILIBRIUM
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
30 by Wardah RI 21032014
PATOFISIOLOGI - DISEQUILIBRIUM
bull Akibat hilangnya input sensoris perifer (seringkali dari vestibular proprioseptif atau visual)
bull Atau karena lesi central pada pusat motorik ( basal ganglia cerebellum dan cortex)
DIAGNOSIS - DISEQUILIBRIUM
a Gait dari ggn cerebellar ggn vestibular ggn sensoris
b Ggn vestibular bilateral disertaitanpa penurunan pendengaran
bull Respon menurun atau (-) pada pemeriksaan stimulasi kalorik dan rotasional
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
31 by Wardah RI 21032014
TERAPI DISEQUILIBRIUM
bull Tx fisik bertuj utk gait amp balance training (melatih otak agar menggunakan signal sensori yg masih bertahan shg dpt mengkompensasi area yg telah rusak)
bull Gait amp balancing training lt bermanfaat pd px dg lesi cerebellum krn cerebellum merupakan kunci refleks2 postural adapting
bull Disequilibrium yg disebabkan ok kel supratentorial (parkinson hidrsefalus) atasi underlying process
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
32 by Wardah RI 21032014
PROGNOSIS
bull Hilangnya sensori perifer (vestibular proprioseptif atau visual) rarr Menyebabkan ggn pola jln rarr Pasien tetap dpt bergerak
(mobile)
bull Penyebab central
bull Infark atau degenerasi cerebelllum
bull Ggn pola jln yg lebih berat
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
33 by Wardah RI 21032014
VERTIGO
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Definisi
Vertigo is defined as a An illusion or hallucination of movement which is usually rotation either of oneself or the environment
This may be a sensation of turning spinning falling rocking etc
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Central (15)
bull Brainstem infarctischemia
bull Tumor
bull Cerebellopontine angle
bull Brainstem
Vertigo acute vestibular asymmetry
Peripheral (85)
bull Benign positional
bull Labyrinthitis
bull Menierersquos
bull Otitis media
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Central
Gradual onset (except stroke)
Persistent
Neuro findings common
Nystagmus any direction - changes with gaze
Nystagmus not suppressable
Unable to stand
Vertigo history and exam
Peripheral
Sudden severe
Episodic
Ear symptoms common
Nystagmus horizontaltorsional no change with gaze
Nystagmus suppressed with fixation
Able to stand lean to lesion
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
37 by Wardah RI 21032014
PATOFISIOLOGI - VERTIGO
bull Ketidak seimbangan tonus vestibular
bull Akibat
bull tdk adanya input perifer karena kerusakan labirin atau nervus vestibular atau
bull disebabkan gangguan aktivitas nuclear vestibular atau vestibulocerebellar unilateral
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
38 by Wardah RI 21032014
bull TX TERBAIK = TX DEFINITIF
bull 2 kategori tx simptomatis
bull Vestibular suppressant
bull Anti emetik
bull Tx vestibular suppressant bekerja pd tk neurotransmitter mempengaruhi impuls2 dari neuron vestibular primer ke sekunder serta mempertahankan tonus nuclei vestibular
bull Bekerja setelah 30 mnt
bull Pemberian im atau iv lebih disukai
bull Es mulut kering dan sedasi
TERAPI SIMPTOMATIS
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
39 by Wardah RI 21032014
CTH VESTIBULAR SUPPRESSANT
1 MECLIZINE 125 ndash 59 mgpo tiap 8 jam
2 DIMENHYDRINATE 25- 100 mg im iv po supp tiap 8 jam
3 SCOPOLAMINE 15 mg transdermal patch tiap 3 hr
4 PROMETHAZINE 125 ndash 50 mg im iv po supp tiap 8 jam
5 LORAZEPAM 05 ndash 2 mg im iv po tiap 8 jam
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
40 by Wardah RI 21032014
OBAT ANTI EMETIK
bull Antagonis dopamin dan kolinergik shg mencegah mual dan muntah pd pusat muntah
bull Efek samping parkinsonism akathisia distonia dan diskinesis
bull Cth
1 PROCHLORPERAZINE 25 ndash 10 mg im iv po supp tap 8 jam
2 METCLOPRAMIDE 5 ndash 10 mg im iv po tiap 8 jam
3 TRIMETHOBENZAMIDE 100 ndash 200 mg im iv po supp tiap 8 jam
4 DROPERIDOLE 25 ndash 10 mg im iv tiap 8 jam
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
41 by Wardah RI 21032014
REHABILITASI VERTIGO
bull Stlh terjadi lesi vestibular perifer akut kompensasi central scr bertahap bekerja dlm beberapa hari
bull Penggunaan vestibular suppresant dan anti emetik dpt mengganggu proses kompensasi shg penggunaannya hendaknya hanya bbrp hari pertama Segera setelah muntah berhenti tx dihentikan scr bertahap utk menstimulasi kompensasi yg normal akan terjadi
bull Program exercise dpt mempercepat prses kompensasi setelah terjadinya lesi vestibular perifer akut
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
42 by Wardah RI 21032014
SAMPEL EXERCISE
bull Fase akut fokus mata amp menghindari gerakan mata yg memprovokasi dizziness
bull Minimalisasi nistagmus dg fixasi 1 target target bergerak
bull Latihan berdiri dan berjalan dkt dinding atau dg asisten
bull Disertai gerakan kepala
bull Proses kompensasi selama 2 ndash 6 bln stlh kerusakan vestibular akut
bull Dizziness yg menetap menunjukkan proses yg sedang berlanjut atau kmpensasi central yg lemah
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
43 by Wardah RI 21032014
BPPV
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Teori BPPV
bull Cupulolithiasis
bull calcific deposits on cupula rendering SCC gravity dependent
bull Canalolithiasis
bull calcific debris in SCC
bull pulling of cupula by plunger-like effect
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
45 by Wardah RI 21032014
bull Kristal calsium carbonat bebas (normalnya dlm macula utricula yg masuk dalam canalis semisircularis posterior)
bull Dg adanya perub posisi kristal berpindah ke dalam endolimfe dan menggeser cupula
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
46
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
47
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
48 by Wardah RI 21032014
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
49 by Wardah RI 21032014
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
50
Causes
bull Idiopathic
bull Infection (viral neuronitis)
bull Head trauma
bull Degeneration of the peripheral end organ
bull Surgical damage to the labyrinth
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
51 by Wardah RI 21032014
DIAGNOSIS
bull Benign kondisi yg tdk terlalu serius atau progresif
bull Paroxysmal onsetnya mendadak dan tdk dpt diprediksi
bull Positional timbul ketika ada perubahan posisi kepala
bull Vertigo menyebabkan keluhan dizziness
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
52
Diagnosis
bull Lab Studies
bull No pathognomonic laboratory test for BPV exists Laboratory tests may be ordered to rule out other pathology
bull Imaging Studies
bull No
bull Procedures
bull The Dix-Hallpike test along with the patients history aids in the diagnosis of BPV
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
53
Treatment
bull Medications
bull The Canalith Repositioning Procedure (CRP)
bull Surgery
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
54
Medications - symptomatic
bull Antiemetic
bull Antihistaminic
bull Anticholinergic
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
55 by Wardah RI 21032014
bull TEGAKKAN DX DG DIX HALLPIKE
bull Manuver repositioning
bull Tk perbaikan meningkat dg pengulangan manuver amp vibrasi pd regio mastoid
bull Nistagmus yg persisten krn
bull Debris menempel pd ddg kanalis semisirkularis
bull Debris terperangkap dlm cupula amp tdk dpt bergerak bebas
bull Saat posisi kepala tergantung ketika manuver kepala jgn elevasi krn partikel dpt menjau dr utricle
bull Vertigo yg timbul ketika kembali ke posisi duduk krn bolus debris otolit jatuh keluar dr kanal menuju utricle
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
56 by Wardah RI 21032014
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
57 by Wardah RI 21032014
MANUVER REPOSITIONING
bull Tingkat keberhasilan 80 setelah 1 sesi terapi dan 100 setelah gt1 sesi Tingkat kekambuhan 30 setelah periode 30 bln
bull Epley manuver
bull Brandt ndash daroff exercise
bull Semont manuver
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
58 by Wardah RI 21032014
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
59 by Wardah RI 21032014
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
60 by Wardah RI 21032014
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
61 by Wardah RI 21032014
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
62 by Wardah RI 21032014
BPV VARIAN HORISONTAL
bull Px digulingkan pd bid canal semisircularis horisontal saat baring supinasi 90deg sisi normal pronasi posisi awal
bull Px berbaring pd sisi telinga yg sehat di bawah utk beberapa jam atau sepanjang malam
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
63 by Wardah RI 21032014
INSTRUKSI DI RUMAH
bull BPV yg sering kambuh manuver di rumah
bull Vibrator massage leher
bull Pd bbrp px debris tdk dpt dihiangkan sempurna terangkan kemungkinan kekambuan dan pasien menghindari posisi ke belakang scr ekstrim (salon dan drgigi) yg akan menyebabkan debris masuk kembali ke canalis semicirkularis posterior
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
64 by Wardah RI 21032014
PEMBEDAHAN (TAMB)
bull Singular neurectomy
bull Vestibular Nerve Section
bull Posterior Canal Plugging Procedure
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
65 by Wardah RI 21032014
PROGNOSIS
bullRemisi spontan stlh beberapa mgg ndash bln
bullKekambuhan
bullInsiden meningkat ~ bertambahnya usia
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
66 by Wardah RI 21032014
Vestibulopathy perifer acute = neuritis vestibular
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
67 by Wardah RI 21032014
PATOFISIOLOGI
bull Epidemik
bull Riw familial
bull Musim semi dan awal musim panas
bull Infeksi virus
bull Atropi pd 1gt serabut saraf vestibular
bull Proses infeksi atau postinfeksi
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
68 by Wardah RI 21032014
DIAGNOSIS
bull Karakteristik klinis vertigo spontan berkepanjangan membaik bertahap dlm bbrp hari
bull Nistagmus unilateral dg fase cepat menjauhi telinga yg sakit amplitudo nistagmus lt ketika melihat ke arah telinga yang sakit
bull Tdk adanya tanda dan gx neurologis lain yang menyertai
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
69 by Wardah RI 21032014
TX SIMPTOMATIS
bull Vestibular suppressant dan anti emetik
bull 2 RCT membandingkan
bull Dimenhydrinate iv (50 mg)
bull Lorazepam 2 mg
bull Dimenhydrinate im (50 mg)
bull Droperidol 25 mg
Utk tx vertigo perifer akut di IRD bull Dimenhydrinate gt efektif dp lorazepam
bull Efektivitas Dimenhydrinate = droperidole
bull Es sedasi (es lt meclizine amp scopolamine transdermal)
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
70 by Wardah RI 21032014
VESTIBULAR EXERCISE
bull Perbaikan memerlukan bbrp minggu
bull Tuj utk akselerasi proses kompensasi vestibular dan memperbaiki tk kesembuhan akhir
bull Kompensasi dpt diakselerasi dg amfetamin dan dihambat dg obat sedasi (diazepam)
bull Latihan gt sering menyebabkan perbaikan yg gt cpt
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
71 by Wardah RI 21032014
STEROID amp OBAT ANTIVIRAL
bull Acyclovir 1 grhr selama 10 hr utk herpes zoster oticus
bull 1 studi placebo ndash controlled berskala kecil pemberian steroid do tinggi akan memberikan efek anti inflamasi dan scr signifikan memperpendek perjalanan penyakit dan derjat berat gx vestibulopathy perifer unilateral akut
bull Acyclovir + steroid do tinggi tdk gt baik dp penggunaan steroid do tinggi saja
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
72 by Wardah RI 21032014
PROGNOSIS
bullMonophasic
bullOnset selama bbrp jam menghilang secara berthp dlm bbrp hari
bull Kembali normal setelah bbrp minggu
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
73 by Wardah RI 21032014
MENIERE SYNDROME
1861
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
74 by Wardah RI 21032014
PATOFISIOLOGI
bull Peningkatan volume endolimfe disertai distensi sistem endolimfatik ( hidrops endolimfatik)
bull Ruptur membran labirin yg dpt menjelaskan adanya keluhan mendadak (merupakan karakteristik sindrom ini)
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
75 by Wardah RI 21032014
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
76 by Wardah RI 21032014
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
77 by Wardah RI 21032014
KEMUNGKINAN ETIOLOGI (TAMB)
bull Anatomical-abnormalities
bull Genetic-autosomal dominant
bull Immunological-immune complex deposition
bull Viral-serum IgE to herpes simples virus types I and II Epstein-Barr virus and CMV
bull Vascular-associated with migraines
bull Metabolic-potassium intoxication
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
78 by Wardah RI 21032014
DIAGNOSIS
bull Ggn pendengaran yg berfluktuatif (terutama utk suara frekuensi yang rendah)
bull menyertai keluhan vertigo yg episodik
bull Ada periode intra-aural fullness
bull Pemeriksaan weber menunjukkan lateralisasi menjauh dari telinga yg sakit
bull Tes rinne menunjukkan konduksi udara lebih baik daripada konduksi tulang
bull Audiometri ECOG ENG
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
79 by Wardah RI 21032014
bull Pembatasan diet garam 1 ndash 2 grr selama 3 bln baik intake garam ditingkatkan bertahap dan monitor ketat gx
bull Hindari mkn yg byk mgd gula dan garam hindari alkohol kopi coklat
bull HCT 50 mg 1 ndash 2 xhr efek tambahan tp tdk dpt menggantikan tx restriksi garam
bull Acetazolamide 250 mg 1 ndash 2 xhr menurunkan tek osmtik dlm telinga (RCT - )
bull Tx profilaksis dg vestibular suppressant utk serangan moderate ndash berat yg lebih sering
bull Vestibular exercise perannya minimal
TERAPI
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
80 by Wardah RI 21032014
PEMBEDAHAN
1 SHUNT ENDOLIMFATIC DUCT amp SAC bull Tdk efektif krn teknik sulit utk mempertahankan
shunt tetap terbuka dlm sistem endolimfe
2 ABLASI bull gt efektif pd px dg ggn unilateral dg kerusakan
pendengaran fungsional bull Vestibular neurectomy utk memelihara fungsi
pendengaran pd px dg fungsi residu cochlear
3 INJ GENTAMYCIN dlm telinga tengah bull Mudah bull Dpt dilakukan dg rawat jalan bull Tdk mempengaruhi prosedur tx definitif
pembedaan lanjutan bull SelektIf utk ototoksisitas vestibular
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
81 by Wardah RI 21032014
PEMBEDAHAN (TAMBAHAN)
bull Vestibular neurectomy
bull Stellate ganglionetomy
bull Labyrinthectomy
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
82 by Wardah RI 21032014
PROGNOSIS
bull Episode berulang
bull Fluktuatif penurunan pendengaran tinitus dan vertigo selama bbrp jam
bull Perjalanan penyakit hilangnya pendengaran unilateral scr progresif dlm bbrp thn hingga mencapai stadium ldquoburnt outrdquo (episode vertigo menghilang)
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
108
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
Rangkuman = Vertigo perifer
Durasi Gejala penyerta
BPPV Detik Perubahan posisi kepala
Menierersquos disease
Menit Tinitus penurunan
pendengaran
Neuritis vestibularis
Jam Flue like syndrome
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
110 by Wardah RI 21032014
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
111 by Wardah RI 21032014
AAO-HNS Committee on Hearing and Equilibrium revised definition in 1995 bull Possible Menieres disease
bull Episodic vertigo of the Menieres type without documented hearing loss or bull Sensorineural hearing loss fluctuating or fixed with dysequilibrium but without
definitive episodes bull Other causes excluded
bull Probable Menieres disease bull One definitive episode of vertigo bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other causes excluded
bull Definite Menieres disease bull Two or more definitive spontaneous episodes of vertigo 20 minutes or longer bull Audiometrically documented hearing loss on at least one occasion bull Tinnitus or aural fullness in the treated ear bull Other cases excluded
bull Certain Menieres disease bull Definite Menieres disease plus histopathologic confirmation
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
112 by Wardah RI 21032014
Definition of Menierersquos
bull Staging of Hearing Loss in DefiniteCertain Menierersquos
Stage Four Tone Average dB
1 lt=25
2 26-40
3 41-70
4 gt70
Committee on Hearing and Equilibrium Guidelines for Diagnoses and Evaluation
of Therapy in Menierersquos Disease AAOHNS Board of Directors March 1994
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
113 by Wardah RI 21032014
Physiology
bull Production and flow of Endolymph - Theories
bull Longitudinal ndash produced in membranous labyrinth flows to endolymphatic sac then to dural venous sinuses
bull Diffuse ndash produced and absorbed along the membranous labyrinth
bull Periodic Flow ndash endolymph flows only with changes in volume or pressure
Andrews JC Intralabyrinthine fluid dynamics Meniere disease 12(5)
Oct 2004 pp408-412
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
114 by Wardah RI 21032014
Medical Management
bull Acute Therapy
bull Relatively non-controversial
Brookes GB The pharmacological treatment of Menierersquos disease Clinical Otolaryngology
21(1) Feb1996 pp3-11
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
115 by Wardah RI 21032014
Endolymphatic Sac Surgery
Coker Newton J et al Atlas of Otologic Surgery WB Saunders
2001
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
116 by Wardah RI 21032014
Vestibular Nerve Section
Coker Newton J et al Atlas of Otologic Surgery WB Saunders 2001
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
117 by Wardah RI 21032014
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
118 by Wardah RI 21032014
Cerebellar stroke (cont)
1 SCA lateral midbrainpons and
superior cerebellum bull vertigo less common
bull ipsi dysmetria
bull ipsi Hornerrsquos
bull contra hearing loss (lateral lemniscus)
2 AICA lateral pons and anterior cerebellum also internal auditory artery
bull vertigo
bull ipsi dysmetria
bull ipsi tinnitushearing loss (often from IAA injury)
bull ipsi V VII Hornerrsquos
3 PICA dorsolateral medulla and posterior medial cerebellum
bull origin Wallenberg syndrome (8)
bull medial branch vertigo ataxia nystagmus
bull lateral branch vertigo ataxia limb dysmetria nystagmus
Timothy Hain MD
From wwwtchaincom
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
119 by Wardah RI 21032014
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff
120 by Wardah RI 21032014
CRP Summary--What to use When
1048715 Posterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont)
ndash Possibly CRP with vibration
ndash Brandt - Daroff
1048715 Anterior BPPV - Cupulothiasis
ndash Liberatory Maneuver (Semont) with initial head position rotated 90 deg
ndash Possibly CRP with vibration
1048715 Horizontal BPPV - Cupulothiasis
ndash Modified Brandt-Daroff