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Paediatric Bell’s Palsy Paediatric Update November 2014 Richard Webster, Paediatric Neurologist Children’s Hospital at Westmead
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Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

May 14, 2020

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Page 1: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Paediatric Bell’s Palsy Paediatric Update November 2014

Richard Webster, Paediatric Neurologist

Children’s Hospital at Westmead

Page 2: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Typical history

Unilateral LMN facial weakness

Acute onset

– over a day or two

– progressive worst within 2-4 weeks

Preceding ear canal pain

Recovery of function

– starts within 3 weeks

– resolution within 6 months

Page 3: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Definition Bell’s palsy

Acute idiopathic peripheral facial nerve palsy

– 1. Assessment

– 2. Differential diagnosis

– 3. Treatment

– 4. Monitoring

Page 4: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

..but first some anatomy

Facial nerve motor nucleus

– Lower pons

– Fibres of VIn curve around the VIIn nucleus

– Bilateral supranuclear inputs for upper face control

Facial nerve

– Leaves pontomedullary junction

– Sensory/autonomic fibres join in facial canal

– Passes through the facial canal

Page 5: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Facial nerve anatomy

Functions of facial nerve – 1. Facial expression

– 2. Lacrimal gland – greater petrosal nerve

– 3. Nerve to stapedius

– 4. Taste fibres to anterior 2/3 tongue (chorda tympani)

– 5. Sensation external auditory meatus

– 6. Salivation – (chorda tympani)

Page 6: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

1. Assessment: facial expression

1. Observe

2. Look up

3. Eye closure

4. Muscles of facial expression

– Smile – emotional/voluntary

– Blow out cheeks – lip closure

5. Platysma

– Difficult

Page 7: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Bell’s palsy algorithm? Facial palsy?

LMN UMN

Page 8: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Face assessment

1. What is weak?

– One side or both sides

– Is it all consistent with VIIn?

2. Is the forehead involved?

– UMN lesions spare the forehead

– Get the child to look up

Page 9: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

1. Where in the nerve is the lesions?

1. Dry eye?

2. Hyperacusis?

3. Loss of taste (difficult in most children) ant 2/3 of tongue

4. Test for auricular sensation

Page 10: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Bell’s palsy algorithm Facial palsy?

LMN UMN

Neurological exam

Isolated Other signs

Page 11: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Is this isolated facial n palsy?

Cranial nerves

– II – papilloedema

– VI + gaze – nuclear lesions

– VIII – hearing

– IX, X – swallowing, palate

– XI,XII

Cerebellum

Long tract signs

Gait

Page 12: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Neurological differential diagnosis

1. Nerve disease

– Infiltration

– Inflammation/infection

– Compression – bone/neoplasm

2. Muscle disease

– Myasthenia

Page 13: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Case

8 yo girl with R LMN VII weakness

– Gradual onset

Treated with steroids for 1/52 no improvement then given a second course

No improvement within 3 weeks

Then developed unsteady gait

– Limitation of eye movement to right

– Deviates to right on tandem gait

Page 14: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Bell’s palsy algorithm Facial palsy?

LMN UMN

Neurological exam

Isolated Other signs

Examination/Ix

No cause

BP - hypertension FBC - leukaemia Middle Ear- OM/mastoiditis, Herpes

Page 15: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Further examination

Check ears

– ? Otitis media

– ? Evidence of vesicles (Ramsay Hunt)

Systemic examination

– BP

– Hepato-splenomegaly/pallor

FBC – evidence of leukaemia

Page 16: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Warning signs

Young age

Bell’s palsy uncommon in infants and young children

3/100,000 < 10, 25/100,00 adults

Malignancy/ diseases predisposing to

malignancy

History of recurrent otitis media

Syndromes associated with facial

dysmorphism

Page 17: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Bell’s palsy algorithm Facial palsy?

LMN UMN

Neurological exam

Isolated Other signs

Examination/Ix

No cause

BP - hypertension FBC - leukaemia Middle Ear- OM/mastoiditis, Herpes

Treat

Page 18: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

3. Treatment

Eye protection

– Avoid corneal abrasions if the patient with facial palsy is unable to close the eye.

– Artificial tears during the day

– Ointment at night

– Eye patch if needed

Page 19: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Treatment

Steroids

– No definite evidence but strong adult data

– Prednisolone 2mg/kg/day (max 60-80mg)

– Give for 5 days and then taper for 5 days

– (Up to date)

Page 20: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Bell’s palsy algorithm Facial palsy?

LMN UMN

Neurological exam

Isolated Other signs

Examination

No cause

BP - hypertension FBC - leukaemia Middle Ear- OM/mastoiditis, Herpes

Treat

Review

Page 21: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

4. When to review?

Review

– 1 week after diagnosis

– Weekly until clear improvement

– Follow-up to make sure of resolution

Page 22: Paediatric Bell s Palsy Paediatric Update November 2014€¦ · Paediatric Bell’s Palsy Paediatric Update November 2014 ... ..but first some anatomy ... Bell’s palsy uncommon

Imaging/referral

Unusual history

– Slow onset

Progression beyond 3 weeks

Failure to improve after 4 weeks

Associated history/signs suggesting a more sinister cause for Bell’s palsy