Major Birth Defects Data from Population-based Birth Defects Surveillance Programs in the United States, 2005-2009 Updated September 2012 Prepared by the National Center on Birth Defects and Developmental Disabilities, Centers for Disease Control and Prevention This report contains data from 41 population-based birth defects programs. These include: Alaska Birth Defects Registry; Arkansas Reproductive Health Monitoring System; Arizona Birth Defects Monitoring Program; California Birth Defects Monitoring Program; Colorado Responds To Children With Special Needs; Connecticut Birth Defects Registry; Delaware Birth Defects Surveillance Project; Florida Birth Defects Registry; Metropolitan Atlanta Congenital Defects Program; Hawaii Birth Defects Program; Iowa Registry For Congenital and Inherited Disorders; Illinois Adverse Pregnancy Outcomes Reporting System; Indiana Birth Defects & Problems Registry; Kentucky Birth Surveillance Registry; Louisiana Birth Defects Monitoring Network; Massachusetts Center For Birth Defects Research And Prevention; Maryland Birth Defects Reporting and Information System; Maine Birth Defects Program; Michigan Birth Defects Registry; Minnesota Birth Defects Information System; Mississippi Birth Defects Registry; Missouri Birth Defects Surveillance System; North Carolina Birth Defects Monitoring Program; North Dakota Birth Defects Monitoring System; Nebraska Birth Defects Registry; New Hampshire Birth Conditions Program; New Jersey Special Child Health Services Registry; Nevada Birth Outcomes Monitoring System; New York State Congenital Malformations Registry; Ohio Connections For Children With Special Needs; Oklahoma Birth Defects Registry; Puerto Rico Birth Defects Surveillance and Prevention System; Rhode Island Birth Defects Program; South Carolina Birth Defects Program; Tennessee Birth Defects Registry; Texas Birth Defects Epidemiology and Surveillance Branch; Utah Birth Defect Network; Virginia Congenital Anomalies Reporting And Education System; Wisconsin Birth Defects Registry; West Virginia Congenital Abnormalities Registry, Education And Surveillance System; and the United States Department of Defense Birth and Infant Health Registry Additional information and program contacts on population-based birth defects surveillance programs are available on page S121. STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S1 Birth Defects Research (Part A) 94:S1-S169 (2012)
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Major Birth Defects Data from Population-based Birth Defects Surveillance Programs in the
United States, 2005-2009
Updated September 2012
Prepared by the National Center on Birth Defects and Developmental Disabilities, Centers for Disease
Control and Prevention
This report contains data from 41 population-based birth defects programs. These include: Alaska Birth
Branch; Utah Birth Defect Network; Virginia Congenital Anomalies Reporting And Education System;
Wisconsin Birth Defects Registry; West Virginia Congenital Abnormalities Registry, Education And
Surveillance System; and the United States Department of Defense Birth and Infant Health Registry
Additional information and program contacts on population-based birth defects surveillance programs
are available on page S121.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S1
Birth Defects Research (Part A) 94:S1-S169 (2012)
AlaskaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)AlaskaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Rectal and large intestinal atresia/stenosis 298.7
.
...
.
.1913.6
529.5
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S2
Birth Defects Research (Part A) 94:S1-S169 (2012)
AlaskaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Reduction deformity, lower limbs 267.8
.
...
.
.1712.1
498.9
Reduction deformity, upper limbs 113.3
.
...
.
.85.7
244.4
Renal agenesis/hypoplasia 288.4
.
...
.
.85.7
448.0
Spina bifida without anencephalus 185.4
.
...
.
.1611.4
356.4
Tetralogy of Fallot 133.9
.
...
.
.1410.0
305.5
Total anomalous pulmonary venous return(TAPVR)
<6.
.
...
.
.<6.
112.0
Transposition of great arteries - All 123.6
.
...
.
.117.9
244.4
Tricuspid valve atresia and stenosis 61.8
.
...
.
.<6.
91.6
Trisomy 13 (Patau syndrome) 61.8
.
...
.
.<6.
81.5
Trisomy 18 (Edwards syndrome) <6.
.
...
.
.<6.
122.2
Ventricular septal defect 24673.6
.
...
.
.270192.7
559102.0
2
Total Live Births 33432.
.
...
.
.14009.
54796.
Total Male Live Births 15754.
.
...
.
.7244.
22998.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S3
Birth Defects Research (Part A) 94:S1-S169 (2012)
AlaskaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)AlaskaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 51
13.73652.5
8715.9
Trisomy 13 (Patau syndrome) <6.
<6.
81.5
Trisomy 18 (Edwards syndrome) <6.
<6.
122.2
Total Live Births 37354.
6859.
54796.
**Total includes unknown maternal age
Notes1.Patent ductus arteriosus - only birth weight =>2500 grams Infants.2.Ventricular septal defect - The ABDR is a passive surevillance system. Reports are not submitted as 'probable'. The ABDR does not conduct caseverification on these reports.
General comments-Alaska conducts surveillance for FAS using FASSNET methodology. Contact the program for data on FAS and FASD.-Cases matched to Alaska birth certificates only; birth cohort 2002-2006 for major anomalies only-Data was indicated by race for non-hispanic White and non-hispanic AK Native only. Live birth numbers were queried from VS data sets and not frompublished VS data as VS does not publish break downs on these two races with indicated ethnicity.-The ABDR does not collect data on still births or terminations; live birth information only.-The ABDR does not collect or provide infomation on amniotic bands.-The ABDR does not provide data to any other state agency for the purpose of further metabolic and/or medical testing.-The ABDR does not provide numbers for cells with <6 cases.-The Alaska Birth Defects Registry collected data during all years of this birth cohort-The Alaska Birth Defects Registry does not provide data on individual years within the birth cohort. Only Totals by Race and Age are presented withindividual year data-The Alaska Birth Defects Registry uses the ICD-9 coding system.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S4
Birth Defects Research (Part A) 94:S1-S169 (2012)
ArizonaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)ArizonaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Anencephalus 211.0
42.1
411.9
10.7
41.3
731.5
Aniridia 10.0
00.0
20.1
00.0
00.0
30.1
Anophthalmia/microphthalmia 100.5
10.5
281.3
10.7
20.6
440.9
Anotia/microtia 150.7
00.0
371.7
32.0
103.2
651.3
Aortic valve stenosis 371.8
21.1
422.0
21.3
61.9
891.8
Biliary atresia 20.1
21.1
60.3
00.0
20.6
120.2
Bladder exstrophy 30.1
00.0
60.3
00.0
00.0
90.2
Choanal atresia 201.0
10.5
170.8
00.0
20.6
420.9
Cleft lip with and without cleft palate 2029.8
137.0
23911.1
1610.5
7223.3
54911.2
Cleft palate without cleft lip 1145.5
73.8
1486.9
149.2
206.5
3106.3
Coarctation of aorta 1095.3
42.1
904.2
63.9
123.9
2254.6
Common truncus 110.5
10.5
110.5
10.7
10.3
260.5
Congenital cataract 80.4
10.5
190.9
00.0
31.0
330.7
Diaphragmatic hernia 381.8
31.6
442.0
21.3
113.6
1002.0
Down syndrome (Trisomy 21) 24812.1
189.7
28013.0
1610.5
3712.0
60812.4
Ebstein anomaly 150.7
00.0
130.6
21.3
51.6
360.7
Encephalocele 100.5
21.1
170.8
21.3
31.0
340.7
Esophageal atresia/tracheoesophagealfistula
432.1
21.1
411.9
00.0
61.9
921.9
Gastroschisis 914.4
52.7
1326.1
32.0
258.1
2655.4
Hirschsprung disease (congenitalmegacolon)
311.5
63.2
231.1
10.7
10.3
641.3
Hypoplastic left heart syndrome 653.2
63.2
512.4
32.0
92.9
1362.8
Omphalocele 331.6
31.6
371.7
63.9
31.0
841.7
Pulmonary valve atresia and stenosis 803.9
63.2
1155.3
63.9
185.8
2304.7
Pulmonary valve atresia 361.8
42.1
502.3
32.0
113.6
1072.2
Reduction deformity, lower limbs 100.5
73.8
251.2
10.7
31.0
471.0
Reduction deformity, upper limbs 341.7
52.7
562.6
21.3
103.2
1112.3
Spina bifida without anencephalus 643.1
73.8
813.8
42.6
113.6
1733.5
Tetralogy of Fallot 793.8
73.8
974.5
53.3
196.1
2124.3
Transposition of great arteries - All 532.6
52.7
422.0
32.0
20.6
1082.2
dextro-Transposition of great arteries(d-TGA)
502.4
52.7
341.6
32.0
20.6
972.0
Trisomy 13 (Patau syndrome) 150.7
42.1
261.2
53.3
31.0
541.1
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S5
Birth Defects Research (Part A) 94:S1-S169 (2012)
ArizonaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Trisomy 18 (Edwards syndrome) 371.8
42.1
401.9
53.3
103.2
972.0
Total Live Births 205619.
18626.
214999.
15253.
30914.
491930.
**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S6
Birth Defects Research (Part A) 94:S1-S169 (2012)
ArizonaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)ArizonaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 340
7.926843.3
60812.4
Trisomy 13 (Patau syndrome) 411.0
121.9
541.1
Trisomy 18 (Edwards syndrome) 631.5
335.3
972.0
Total Live Births 429859.
61931.
491930.
**Total includes unknown maternal age
General comments-In this data submission, ABDMP adhered to the requested race/Hispanic categories. However, for traditional in-state reports ABDMP categorizes Whitesas Hispanic or non-Hispanic, and for other races (i.e. Black, Asian, and American Indian) retains the single race code regardless of their Hispanicdesignation.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S7
Birth Defects Research (Part A) 94:S1-S169 (2012)
ArkansasBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)ArkansasBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
ArkansasBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 886.5
266.7
157.0
37.1
327.0
1356.7
Pulmonary valve atresia and stenosis 18613.7
5614.4
2411.2
921.3
19.0
27613.7
Pulmonary valve atresia 90.7
30.8
10.5
12.4
00.0
140.7
Pyloric stenosis 26919.8
348.7
6028.0
24.7
327.0
36818.2
Rectal and large intestinal atresia/stenosis 957.0
287.2
2511.7
614.2
19.0
1557.7
Reduction deformity, lower limbs 372.7
164.1
41.9
00.0
00.0
572.8
Reduction deformity, upper limbs 614.5
153.9
125.6
49.5
00.0
924.6
Renal agenesis/hypoplasia 272.0
123.1
83.7
00.0
00.0
472.3
Spina bifida without anencephalus 725.3
61.5
136.1
00.0
00.0
914.5
Tetralogy of Fallot 644.7
153.9
73.3
12.4
00.0
874.3
Total anomalous pulmonary venous return(TAPVR)
131.0
51.3
20.9
12.4
19.0
221.1
Transposition of great arteries - All 664.9
112.8
62.8
12.4
00.0
844.2
dextro-Transposition of great arteries(d-TGA)
604.4
102.6
52.3
12.4
00.0
763.8
Tricuspid valve atresia 60.4
30.8
41.9
00.0
00.0
130.6
Trisomy 13 (Patau syndrome) 141.0
41.0
20.9
00.0
00.0
201.0
Trisomy 18 (Edwards syndrome) 372.7
143.6
10.5
00.0
00.0
522.6
Ventricular septal defect 85663.0
15840.6
15974.2
2559.1
544.9
120359.6
Total Live Births 135927.
38898.
21430.
4228.
1113.
201763.
Total Male Live Births 69974.
19684.
10822.
2166.
553.
103282.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S9
Birth Defects Research (Part A) 94:S1-S169 (2012)
ArkansasTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)ArkansasTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 142
7.69963.5
24212.0
Trisomy 13 (Patau syndrome) 140.8
63.8
201.0
Trisomy 18 (Edwards syndrome) 301.6
2214.1
522.6
Total Live Births 186100.
15602.
201763.
**Total includes unknown maternal age
General comments-Stillborns include fetal losses at any gestational age and subjects where outcome is unknown.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S10
Birth Defects Research (Part A) 94:S1-S169 (2012)
CaliforniaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)CaliforniaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Rectal and large intestinal atresia/stenosis 303.3
*.
813.9
127.5
*.
1424.1
5
Reduction deformity, lower limbs 131.4
*.
251.2
*.
*.
461.3
Reduction deformity, upper limbs 252.8
74.5
592.8
74.4
*.
1043.0
Renal agenesis/hypoplasia 111.2
00.0
321.5
53.1
*.
501.4
6
Spina bifida without anencephalus 252.8
*.
934.4
*.
00.0
1424.1
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S11
Birth Defects Research (Part A) 94:S1-S169 (2012)
CaliforniaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total*** Notes
Tetralogy of Fallot 273.0
*.
663.1
53.1
00.0
1023.0
Total anomalous pulmonary venous return(TAPVR)
91.0
00.0
351.7
*.
00.0
471.4
dextro-Transposition of great arteries(d-TGA)
212.3
*.
341.6
*.
00.0
611.8
Tricuspid valve atresia 91.0
00.0
140.7
*.
*.
250.7
Trisomy 13 (Patau syndrome) 70.8
*.
211.0
*.
00.0
431.2
Trisomy 18 (Edwards syndrome) 161.8
53.2
522.5
*.
*.
1012.9
Total Live Births 89951.
15616.
209751.
15999.
2614.
345349.
Total Male Live Births 46356.
8026.
106684.
8234.
1339.
176557.
*Cell size suppressed to protect confidentiality or to indicate case count <5**Hypospadias: prevalence per 10,000 male live births***Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S12
Birth Defects Research (Part A) 94:S1-S169 (2012)
CaliforniaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)CaliforniaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total*** NotesDown syndrome (Trisomy 21) 254
8.322258.7
48814.1
Trisomy 13 (Patau syndrome) 240.8
112.9
431.2
Trisomy 18 (Edwards syndrome) 441.4
4211.1
1012.9
Total Live Births 307458.
37847.
345349.
***Total includes unknown maternal age
Notes1.ASD: 1) only cases confirmed by physician review or echo or cath or surgery or autopsy are included; 2) if the ASD is a component of another majorheart malformation, it is not counted2.Submucous cleft and bifid uvula are not included in this report.3.Isolated tracheoesophageal fistula is not included in this report.4.Hypospadias case counts include only 2nd and 3rd degree.5.Anal stenosis is not included in this report.6.Unilateral renal agenesis/hypoplasia is not included in this report.
General comments-Cases with chromosomal defects other than trisomy 13, 18 and 21 are not included in this report.-Cases with single gene disorders are not included in this report.-Stillbirth > = 20 wks is included for all defect types.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S13
Birth Defects Research (Part A) 94:S1-S169 (2012)
ColoradoBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)ColoradoBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
ColoradoBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia 361.7
74.6
302.7
21.7
00.0
762.2
Pyloric stenosis 27713.3
159.8
18817.1
43.5
416.2
48914.0
Rectal and large intestinal atresia/stenosis 1165.6
74.6
807.3
65.2
28.1
2196.3
Reduction deformity, lower limbs 371.8
21.3
111.0
10.9
14.1
551.6
Reduction deformity, upper limbs 562.7
42.6
343.1
10.9
14.1
1073.1
Renal agenesis/hypoplasia 1155.5
95.9
484.4
21.7
14.1
1935.5
Spina bifida without anencephalus 683.3
21.3
423.8
21.7
14.1
1213.5
6
Tetralogy of Fallot 864.1
95.9
423.8
97.8
00.0
1464.2
Total anomalous pulmonary venous return(TAPVR)
150.7
10.7
211.9
21.7
00.0
411.2
Transposition of great arteries - All 592.8
63.9
343.1
32.6
14.1
1073.1
dextro-Transposition of great arteries(d-TGA)
391.9
32.0
171.5
21.7
00.0
641.8
Tricuspid valve atresia and stenosis 251.2
53.3
222.0
21.7
00.0
561.6
7
Trisomy 13 (Patau syndrome) 271.3
10.7
60.5
00.0
28.1
942.7
Trisomy 18 (Edwards syndrome) 391.9
32.0
292.6
32.6
00.0
1634.7
Ventricular septal defect 92144.4
7549.2
54349.4
3933.7
1040.6
161446.2
8
Total Live Births 207564.
15254.
109893.
11580.
2463.
349062.
Total Male Live Births 106639.
7810.
56394.
5896.
1217.
179134.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S15
Birth Defects Research (Part A) 94:S1-S169 (2012)
ColoradoTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)ColoradoTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 300
10.239572.1
74321.3
Trisomy 13 (Patau syndrome) 411.4
458.2
942.7
Trisomy 18 (Edwards syndrome) 682.3
7814.2
1634.7
Total Live Births 294218.
54818.
349062.
**Total includes unknown maternal age
Notes1.Anencephalus: live births and fetal deaths any gestational age2.Atrioventricular septal defect:Cannot include Inlet VSD3.Gastroschisis: medical record review4.Omphalocele: medical record review5.Patent ductus arteriosus: birth weight greater than or equal to 2500 grams6.Spina bifidia without anencephalus: live birth and fetal deaths any gestational age7.Tricuspid valve atresia and stenosis:Tricuspid stenosis and hypoplasia included8.Ventricular septal defects: includes probable cases
General comments-Contact State Program directly in regards to fetal alcohol syndrome-CDPHE disclaims responsibility for any analysis, interpretations, or conclusions
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S16
Birth Defects Research (Part A) 94:S1-S169 (2012)
ConnecticutBirth Defects Counts and Prevalence 2005-2008 (Prevalence per 10,000 Live Births)ConnecticutBirth Defects Counts and Prevalence 2005-2008 (Prevalence per 10,000 Live Births)
ConnecticutBirth Defects Counts and Prevalence 2005-2008 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia and stenosis 565.7
2110.6
267.7
11.1
00.0
1096.6
Pyloric stenosis 23523.7
3316.6
12837.8
1213.4
00.0
41124.8
Rectal and large intestinal atresia/stenosis 292.9
94.5
154.4
11.1
00.0
553.3
Reduction deformity, lower limbs 121.2
31.5
30.9
22.2
00.0
211.3
Reduction deformity, upper limbs 202.0
42.0
51.5
22.2
00.0
321.9
Renal agenesis/hypoplasia 535.4
73.5
226.5
22.2
00.0
845.1
Spina bifida without anencephalus 161.6
21.0
72.1
11.1
00.0
271.6
Tetralogy of Fallot 565.7
115.5
216.2
55.6
00.0
955.7
Transposition of great arteries - All 404.0
73.5
216.2
44.5
00.0
724.4
Tricuspid valve atresia and stenosis 70.7
00.0
20.6
00.0
00.0
90.5
Trisomy 13 (Patau syndrome) 50.5
21.0
20.6
00.0
00.0
90.5
Trisomy 18 (Edwards syndrome) 70.7
21.0
30.9
22.2
00.0
140.8
Ventricular septal defect 47247.7
10251.3
13640.1
8594.9
224.7
80648.7
Total Live Births 98952.
19871.
33905.
8953.
811.
165496.
Total Male Live Births 50548.
10184.
17414.
4590.
432.
84665.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S18
Birth Defects Research (Part A) 94:S1-S169 (2012)
ConnecticutTrisomy Counts and Prevalence by Maternal Age 2005-2008 (Prevalence per 10,000 Live Births)ConnecticutTrisomy Counts and Prevalence by Maternal Age 2005-2008 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 111
8.511031.2
22213.4
Trisomy 13 (Patau syndrome) 40.3
51.4
90.5
Trisomy 18 (Edwards syndrome) 90.7
51.4
140.8
Total Live Births 130250.
35240.
165496.
**Total includes unknown maternal age
General comments-Coding system used is ICD-9
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S19
Birth Defects Research (Part A) 94:S1-S169 (2012)
DelawareBirth Defects Counts and Prevalence 2007-2008 (Prevalence per 10,000 Live Births)DelawareBirth Defects Counts and Prevalence 2007-2008 (Prevalence per 10,000 Live Births)
DelawareBirth Defects Counts and Prevalence 2007-2008 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 118.5
1218.6
38.0
00.0
00.0
2610.7
7
Pulmonary valve atresia and stenosis 2217.0
1218.6
12.7
19.5
00.0
3614.8
8
Pulmonary valve atresia 10.8
11.6
12.7
00.0
00.0
31.2
8
Pyloric stenosis 129.3
23.1
718.7
218.9
00.0
249.9
Rectal and large intestinal atresia/stenosis 96.9
23.1
00.0
00.0
00.0
124.9
Reduction deformity, lower limbs 00.0
23.1
00.0
00.0
00.0
20.8
Reduction deformity, upper limbs 53.9
00.0
00.0
00.0
00.0
52.1
Renal agenesis/hypoplasia 86.2
57.8
25.3
19.5
00.0
166.6
Spina bifida without anencephalus 32.3
34.7
12.7
00.0
00.0
83.3
9
Tetralogy of Fallot 96.9
23.1
25.3
218.9
00.0
156.2
10
Total anomalous pulmonary venous return(TAPVR)
10.8
11.6
00.0
00.0
00.0
20.8
Transposition of great arteries - All 32.3
11.6
38.0
00.0
00.0
72.9
dextro-Transposition of great arteries(d-TGA)
32.3
11.6
38.0
00.0
00.0
72.9
Tricuspid valve atresia 00.0
11.6
00.0
00.0
00.0
10.4
Trisomy 13 (Patau syndrome) 00.0
11.6
00.0
00.0
00.0
10.4
Trisomy 18 (Edwards syndrome) 21.5
23.1
12.7
19.5
00.0
62.5
Ventricular septal defect 9774.9
4163.7
3490.7
218.9
1303.0
17773.0
11
Total Live Births 12955.
6440.
3749.
1057.
33.
24260.
Total Male Live Births 6624.
3260.
1875.
564.
16.
12353.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S21
Birth Defects Research (Part A) 94:S1-S169 (2012)
DelawareTrisomy Counts and Prevalence by Maternal Age 2007-2008 (Prevalence per 10,000 Live Births)DelawareTrisomy Counts and Prevalence by Maternal Age 2007-2008 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 17
8.11338.9
3213.2
Trisomy 13 (Patau syndrome) 10.5
00.0
10.4
Trisomy 18 (Edwards syndrome) 21.0
412.0
62.5
Total Live Births 20922.
3338.
24260.
**Total includes unknown maternal age
Notes1.Trivial or limited are not included.2.Atrial septal fenestrations are reported as an atrial septal defect (ASD). ASDs that self-close (not present after a month) are considered Patent ForamenOvales (PFO). PFOs are not counted.3.Pierre Robin sequence defects are included as a cleft palate.4.Benign external hydrocephalus or hydrocephalus due to a secondary cause are not included.5.Head circumference must be less than the 5th percentile.6.All obstructive and non-obstructive genitourinary defects (i.e., all hydronephrosis and other types of kidney dilation) are included as well as all resolveddefects.7.The newborn must weigh 2500 grams or greater and the PDA must be present at one month of age.8.Peripheral, branch, trivial, or limited are not included.9.Spina bifida occulta is not included.10.A ventricular septal defect with an overriding aorta is counted as Tetralogy of Fallot.11.All sizes and types of ventricular septal defects are included and all resolved VSDs are included.
General comments-2007 Maternal Fetal Medicine cases were derived from cytogenetic lists and fetal therapy lists. 2008 Maternal Fetal Medicine cases were derived fromall possible defect cases handled by MFM.-All chromosomal defects require a cytogenetics report.-All defects found prenatally must be confirmed postnatally or through cytogenetic testing.-All heart defects require an echocardiogram report.-Coding System used was CDC/BPA.-Registry does not distinguish spontaneous terminations from elective terminations. Stillbirths, miscarriages, and terminations are all currently reportedtogether.-Registry was not collecting data in 2005 and 2006. Registry data from 2009 is currently being vetted.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S22
Birth Defects Research (Part A) 94:S1-S169 (2012)
FloridaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)FloridaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Rectal and large intestinal atresia/stenosis 2344.5
1174.8
1153.5
134.1
00.0
4904.3
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S23
Birth Defects Research (Part A) 94:S1-S169 (2012)
FloridaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Reduction deformity, lower limbs 761.5
441.8
451.4
31.0
00.0
1701.5
Reduction deformity, upper limbs 1252.4
492.0
521.6
31.0
00.0
2312.0
Renal agenesis/hypoplasia 2304.5
1014.1
1093.3
92.9
14.0
4614.0
Spina bifida without anencephalus 1523.0
753.1
972.9
20.6
00.0
3292.9
1
Tetralogy of Fallot 2865.6
1285.2
1263.8
144.5
14.0
5664.9
Total anomalous pulmonary venous return(TAPVR)
380.7
251.0
270.8
61.9
00.0
980.9
Transposition of great arteries - All 2665.2
1194.8
1514.5
82.5
00.0
5514.8
dextro-Transposition of great arteries(d-TGA)
1633.2
401.6
792.4
31.0
00.0
2902.5
Tricuspid valve atresia and stenosis 741.4
291.2
331.0
31.0
00.0
1411.2
2
Trisomy 13 (Patau syndrome) 440.9
301.2
240.7
00.0
00.0
1000.9
1
Trisomy 18 (Edwards syndrome) 751.5
542.2
531.6
41.3
00.0
1891.6
1
Ventricular septal defect 279654.3
126751.5
192357.9
12640.1
936.2
621054.0
2
Total Live Births 514599.
245888.
331910.
31389.
2483.
1150397.
Total Male Live Births 263432.
125364.
170036.
16192.
1289.
588624.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S24
Birth Defects Research (Part A) 94:S1-S169 (2012)
FloridaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)FloridaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 783
8.071342.5
149613.0
1
Trisomy 13 (Patau syndrome) 710.7
291.7
1000.9
1
Trisomy 18 (Edwards syndrome) 1091.1
804.8
1891.6
1
Total Live Births 982505.
167823.
1150397.
**Total includes unknown maternal age
Notes1.FL reports live births only2.Includes probable cases3.Cases of Gastroschisis were differentiated from omphalocele by using 54.71 procedure code
General comments-The Florida Birth Defect Registry is a passive population based surveillance system. In 2008, the data linkage methodology was modified to improve caseascertainment. In 2009, the linking methodology was again modified with the addition of Infant Death Certificate as a data source and the elimination ofthree data sources from the department's Children's Medical Services program. These modifications may affect the observed counts and rates.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S25
Birth Defects Research (Part A) 94:S1-S169 (2012)
GeorgiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)GeorgiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
GeorgiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 27233.7
25524.4
18729.8
2213.3
7231.0
76828.2
1
Pulmonary valve atresia and stenosis 496.1
858.1
396.2
127.2
133.0
1957.2
Pulmonary valve atresia 91.1
232.2
121.9
31.8
00.0
501.8
Pyloric stenosis 13817.1
646.1
11117.7
84.8
00.0
33912.5
Rectal and large intestinal atresia/stenosis 243.0
363.4
355.6
84.8
00.0
1114.1
Reduction deformity, lower limbs 151.9
222.1
121.9
00.0
00.0
521.9
Reduction deformity, upper limbs 141.7
323.1
142.2
10.6
00.0
692.5
Renal agenesis/hypoplasia 496.1
494.7
264.1
21.2
133.0
1355.0
Spina bifida without anencephalus 374.6
383.6
284.5
31.8
00.0
1154.2
Tetralogy of Fallot 374.6
504.8
152.4
74.2
00.0
1174.3
Total anomalous pulmonary venous return(TAPVR)
70.9
90.9
101.6
21.2
00.0
291.1
Transposition of great arteries - All 283.5
323.1
152.4
42.4
00.0
823.0
dextro-Transposition of great arteries(d-TGA)
263.2
262.5
121.9
42.4
00.0
712.6
Tricuspid valve atresia and stenosis 101.2
262.5
91.4
21.2
00.0
542.0
Tricuspid valve atresia 60.7
212.0
61.0
21.2
00.0
361.3
Trisomy 13 (Patau syndrome) 111.4
212.0
20.3
00.0
00.0
411.5
Trisomy 18 (Edwards syndrome) 313.8
333.2
132.1
84.8
00.0
1053.9
Ventricular septal defect 54667.6
43741.8
36858.6
4024.1
7231.0
145653.5
Total Live Births 80810.
104606.
62812.
16583.
303.
272284.
Total Male Live Births 41765.
53672.
32506.
8718.
166.
140500.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S27
Birth Defects Research (Part A) 94:S1-S169 (2012)
GeorgiaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)GeorgiaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 234
10.422045.7
45616.7
Trisomy 13 (Patau syndrome) 251.1
163.3
411.5
Trisomy 18 (Edwards syndrome) 361.6
6814.1
1053.9
Total Live Births 224092.
48192.
272284.
**Total includes unknown maternal age
Notes1.Cases included if gestational age =>36 weeks at birth and PDA is present at or beyond 6 weeks of age, or if PDA is present with other heart defectsregardless of gestational age at birth.
General comments-All totals include definite and probable/possible diagnoses.-All totals include live births and stillbirths >= 20 weeks, elective terminations at any gestational age, and prenatal diagnoses with undocumented outcomeat any gestational age.-All totals include prenatal diagonses.-NCHS bridged race data were not available. Multiple-race individuals are included in the totals only.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S28
Birth Defects Research (Part A) 94:S1-S169 (2012)
HawaiiBirth Defects Counts and Prevalence 2005 (Prevalence per 10,000 Live Births)HawaiiBirth Defects Counts and Prevalence 2005 (Prevalence per 10,000 Live Births)
HawaiiBirth Defects Counts and Prevalence 2005 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 3084.8
20489.0
4481.9
153125.8
274.1
224125.0
2
Pulmonary valve atresia and stenosis 822.6
7171.1
1120.5
2722.2
00.0
4625.7
Pyloric stenosis 12.8
00.0
00.0
32.5
00.0
84.5
Rectal and large intestinal atresia/stenosis 12.8
124.4
00.0
64.9
00.0
84.5
Reduction deformity, lower limbs 12.8
00.0
00.0
10.8
00.0
21.1
Reduction deformity, upper limbs 38.5
00.0
00.0
21.6
00.0
52.8
Renal agenesis/hypoplasia 12.8
124.4
00.0
32.5
00.0
73.9
Spina bifida without anencephalus 38.5
00.0
00.0
32.5
00.0
63.3
Tetralogy of Fallot 00.0
248.9
00.0
21.6
00.0
42.2
Total anomalous pulmonary venous return(TAPVR)
12.8
124.4
00.0
10.8
00.0
31.7
Transposition of great arteries - All 12.8
00.0
00.0
54.1
00.0
73.9
Tricuspid valve atresia and stenosis 00.0
00.0
00.0
00.0
00.0
00.0
Trisomy 13 (Patau syndrome) 00.0
00.0
00.0
00.0
00.0
00.0
Trisomy 18 (Edwards syndrome) 12.8
00.0
00.0
21.6
00.0
31.7
Ventricular septal defect 514.1
6146.7
1120.5
5847.7
00.0
7743.0
3
Total Live Births 3539.
409.
83.
12158.
270.
17922.
Total Male Live Births 1361.
348.
27.
6673.
142.
9275.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S30
Birth Defects Research (Part A) 94:S1-S169 (2012)
HawaiiTrisomy Counts and Prevalence by Maternal Age 2005 (Prevalence per 10,000 Live Births)HawaiiTrisomy Counts and Prevalence by Maternal Age 2005 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 7
4.7928.5
168.9
Trisomy 13 (Patau syndrome) 00.0
00.0
00.0
Trisomy 18 (Edwards syndrome) 21.4
13.2
31.7
Total Live Births 14762.
3159.
17922.
**Total includes unknown maternal age
Notes1.Omphalocele and Gastroschisis are reported separately as distinguished from active case ascertainment and by CDC/BPA codes.2.Patent ductus arteriosus: Infants that weigh <2500 grams are excluded.3.Ventricular septal defect: probable cases are included.
General comments-2006-2009 data were not included in this report; however as of 2011, active case ascertainment is in progress for these years.-Data includes stillbirths >/= 20 weeks gestational age.-No major methodological changes to report during the period of 2005. Data collection completed by staff filling out an electronic file/report on laptopat facility.-Pregnancies electively terminated after prenatal diagnosis are included in surveillance data regardless of the gestational age at which they wereterminated.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S31
Birth Defects Research (Part A) 94:S1-S169 (2012)
IllinoisBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)IllinoisBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
IllinoisBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 102321.8
33521.8
42719.9
6613.9
00.0
189121.3
1
Pulmonary valve atresia and stenosis 1362.9
523.4
432.0
71.5
00.0
2442.7
Pulmonary valve atresia 220.5
70.5
80.4
20.4
00.0
400.5
Pyloric stenosis 280.6
40.3
80.4
00.0
00.0
400.5
Rectal and large intestinal atresia/stenosis 1523.2
553.6
793.7
194.0
18.5
3123.5
Reduction deformity, lower limbs 781.7
241.6
221.0
40.8
216.9
1331.5
Reduction deformity, upper limbs 1362.9
493.2
492.3
81.7
216.9
2492.8
Renal agenesis/hypoplasia 2074.4
583.8
904.2
112.3
00.0
3734.2
Spina bifida without anencephalus 1302.8
342.2
653.0
61.3
433.8
2432.7
Tetralogy of Fallot 1302.8
614.0
552.6
173.6
00.0
2713.1
Total anomalous pulmonary venous return(TAPVR)
220.5
80.5
200.9
51.1
00.0
560.6
Transposition of great arteries - All 1372.9
352.3
512.4
122.5
00.0
2432.7
dextro-Transposition of great arteries(d-TGA)
721.5
181.2
251.2
51.1
00.0
1241.4
Tricuspid valve atresia and stenosis 671.4
281.8
341.6
40.8
00.0
1351.5
Tricuspid valve atresia 631.3
261.7
251.2
40.8
00.0
1201.4
Trisomy 13 (Patau syndrome) 591.3
181.2
221.0
10.2
216.9
1041.2
Trisomy 18 (Edwards syndrome) 1022.2
412.7
432.0
61.3
433.8
1982.2
Ventricular septal defect 175237.4
45429.6
85839.9
10221.5
00.0
322836.4
Total Live Births 468624.
153630.
214912.
47544.
1183.
887616.
Total Male Live Births 358043.
134849.
190622.
24383.
602.
709479.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S33
Birth Defects Research (Part A) 94:S1-S169 (2012)
IllinoisTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)IllinoisTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 541
7.258342.3
115013.0
Trisomy 13 (Patau syndrome) 620.8
302.2
1041.2
Trisomy 18 (Edwards syndrome) 700.9
846.1
1982.2
Total Live Births 749761.
137749.
887616.
**Total includes unknown maternal age
Notes1.Only includes cases where the birth weight >=2500g
General comments-Illinois is under court order that strictly limits the data that can be collected about a termination. The birth defect registry is therefore unable to obtainbirth defect information-In 2009, Illinois reduced the number of charts that were reviewed for birth defects, dropping primarily children with very low-birth weights and noreported associated birth defects
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S34
Birth Defects Research (Part A) 94:S1-S169 (2012)
IndianaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)IndianaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
IndianaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia and stenosis 2427.6
417.5
194.9
77.5
112.0
3157.2
Pyloric stenosis 88227.5
6812.4
9625.0
66.4
448.1
107524.6
Rectal and large intestinal atresia/stenosis 1514.7
132.4
184.7
55.4
112.0
1894.3
Reduction deformity, lower limbs 441.4
101.8
92.3
11.1
00.0
651.5
Reduction deformity, upper limbs 752.3
81.5
133.4
11.1
00.0
972.2
Renal agenesis/hypoplasia 1063.3
91.6
153.9
11.1
112.0
1333.0
Spina bifida without anencephalus 1434.5
152.7
215.5
11.1
00.0
1834.2
7
Tetralogy of Fallot 963.0
142.6
143.6
22.1
00.0
1293.0
Total anomalous pulmonary venous return(TAPVR)
210.7
40.7
30.8
00.0
00.0
290.7
Transposition of great arteries - All 1494.7
203.6
143.6
00.0
00.0
1904.4
8
Tricuspid valve atresia and stenosis 260.8
40.7
41.0
00.0
00.0
340.8
9
Trisomy 13 (Patau syndrome) 130.4
30.5
51.3
00.0
00.0
220.5
Trisomy 18 (Edwards syndrome) 351.1
101.8
10.3
00.0
112.0
491.1
Ventricular septal defect 131240.9
13624.8
13434.9
4245.0
00.0
164837.7
10
Total Live Births 320405.
54843.
38409.
9325.
832.
436733.
Total Male Live Births 163976.
27314.
19413.
4852.
396.
223437.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S36
Birth Defects Research (Part A) 94:S1-S169 (2012)
IndianaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)IndianaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 346
8.717847.6
52412.0
Trisomy 13 (Patau syndrome) 190.5
30.8
220.5
Trisomy 18 (Edwards syndrome) 360.9
133.5
491.1
Total Live Births 399093.
37428.
436733.
**Total includes unknown maternal age
Notes1.Ancephalus: Indiana does not collect or report information on stillbirths or terminations. Data reported is based on livebirths (2005-2009).2.Atrial septal defect: A more stringent classification was recently adopted. This classification was only applied to 2005 data.3.Atrioventricular septal defect: Data does not distinguish BPA code 745.487 (2005-2009).4.Prior to July 2009, all children reported with either hypospadias or epispadias were reviewed for a combined disorder of 'hypospadias/epispadias.' Sincethat time our system was modified and children are currently reviewed for hypospadius and epispadias separately.5.Indiana utilizes BPA codes to differentiate gastroschisis from omphalocele.6.Patent ductus arterious: Data reported for children who were gestational age e 36 weeks at birth and whose PDA was last noted at e 6 weeks of age(2005-2009). Unable to exclude < 2500 grams infants.7.Spina bifida with anencephalus: Indiana does not collect or report information on stillbirths or terminations. Data reported is based on livebirths(2005-2009).8.Transposition of great arteries: Data includes entire coding range of 745.10 - 745.19 (2005-2009).9.Tricuspid valve atresia and stenosis: Data does not distinguish BPA codes 746.105 or 746.106 (2005-2009).10.Ventricular septal defect: Data does not distinguish BPA code 745.487 (2005-2009). Probable cases included.
General comments-Birth defects rates based on fewer than 20 cases are unstable.-Case ascertainment in Indiana is a combination of passive ascertainment by electronic submission of hospital discharge information and activeascertainment through chart auditing of 45 targeted conditions identified trhough hospital discharge ICD-9-CM codes.-Data includes children whose conditions were classified with a status of either 'confirmed' or 'probable' based on the abstracted information.-Report based on data as of 08/16/2012. As additional information is constantly entering the system, updated data for birth years 2006-2009 will besubmitted, along with 2010 data, in the next report.-The IBDPR changed how maternal residency was defined in 2012
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S37
Birth Defects Research (Part A) 94:S1-S169 (2012)
IowaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)IowaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
IowaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 46527.5
1518.4
5734.9
1429.6
439.1
55727.8
Pulmonary valve atresia and stenosis 19611.6
911.1
116.7
612.7
219.6
22511.2
Pulmonary valve atresia 221.3
22.5
10.6
12.1
00.0
261.3
Pyloric stenosis 43525.7
1417.2
3622.1
12.1
439.1
49124.5
Rectal and large intestinal atresia/stenosis 774.6
44.9
159.2
36.3
00.0
994.9
Reduction deformity, lower limbs 332.0
56.1
31.8
24.2
00.0
432.1
Reduction deformity, upper limbs 704.1
89.8
106.1
24.2
19.8
914.5
Renal agenesis/hypoplasia 1257.4
67.4
95.5
510.6
00.0
1467.3
Spina bifida without anencephalus 764.5
78.6
138.0
24.2
19.8
994.9
Tetralogy of Fallot 684.0
22.5
106.1
12.1
00.0
824.1
Total anomalous pulmonary venous return(TAPVR)
211.2
00.0
21.2
00.0
19.8
241.2
Transposition of great arteries - All 573.4
22.5
31.8
24.2
00.0
643.2
dextro-Transposition of great arteries(d-TGA)
472.8
11.2
31.8
24.2
00.0
532.6
Tricuspid valve atresia and stenosis 412.4
11.2
31.8
00.0
19.8
472.3
Tricuspid valve atresia 201.2
11.2
21.2
00.0
19.8
241.2
Trisomy 13 (Patau syndrome) 301.8
11.2
31.8
12.1
00.0
351.7
Trisomy 18 (Edwards syndrome) 513.0
33.7
63.7
12.1
00.0
613.0
Ventricular septal defect 92354.6
3543.0
8552.1
1838.0
878.2
107153.4
Total Live Births 169001.
8144.
16324.
4734.
1023.
200585.
Total Male Live Births 86711.
4133.
8353.
2395.
533.
102811.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S39
Birth Defects Research (Part A) 94:S1-S169 (2012)
IowaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)IowaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 165
9.213763.0
30315.1
Trisomy 13 (Patau syndrome) 241.3
115.1
351.7
Trisomy 18 (Edwards syndrome) 331.8
2812.9
613.0
Total Live Births 178826.
21748.
200585.
**Total includes unknown maternal age
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S40
Birth Defects Research (Part A) 94:S1-S169 (2012)
KentuckyBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)KentuckyBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
KentuckyBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 166169.9
356137.0
9266.1
1949.1
<5.
215075.9
2
Pulmonary valve atresia and stenosis 1817.6
197.3
75.0
<5.
00.0
2097.4
Pyloric stenosis 87636.9
4216.2
2215.8
<5.
<5.
95233.6
Rectal and large intestinal atresia/stenosis 1225.1
207.7
75.0
512.9
00.0
1615.7
Reduction deformity, lower limbs 371.6
<5.
<5.
00.0
00.0
471.7
Reduction deformity, upper limbs 431.8
<5.
<5.
<5.
<5.
511.8
Renal agenesis/hypoplasia 873.7
83.1
<5.
<5.
00.0
1023.6
Spina bifida without anencephalus 863.6
114.2
<5.
00.0
00.0
1013.6
Tetralogy of Fallot 803.4
93.5
<5.
00.0
00.0
923.2
Total anomalous pulmonary venous return(TAPVR)
71.5
00.0
00.0
00.0
00.0
71.3
Transposition of great arteries - All 893.7
103.8
53.6
<5.
00.0
1083.8
Tricuspid valve atresia and stenosis 220.9
<5.
<5.
<5.
00.0
260.9
Trisomy 13 (Patau syndrome) 190.8
00.0
<5.
00.0
00.0
250.9
Trisomy 18 (Edwards syndrome) 341.4
62.3
<5.
00.0
00.0
501.8
Ventricular septal defect 104143.8
14254.6
6345.2
1538.7
00.0
130946.2
3
Total Live Births 237656.
25992.
13924.
3872.
358.
283168.
Total Male Live Births 121695.
13215.
7070.
2008.
187.
144867.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S42
Birth Defects Research (Part A) 94:S1-S169 (2012)
KentuckyTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)KentuckyTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 213
8.313549.5
35612.6
Trisomy 13 (Patau syndrome) 180.7
62.2
250.9
Trisomy 18 (Edwards syndrome) 331.3
114.0
501.8
Total Live Births 255588.
27252.
283168.
**Total includes unknown maternal age
Notes1.Atrial septal defect: Probable cases are included2.Patent ductus arteriosus: includes only babies over 2500 g3.Ventricular septal defect: Probable cases are included
General comments-2007-2009 data is preliminary-Although some terminations are issued stillbirth certificates, we do not collect data about terminations-Use ICD-9 codes
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S43
Birth Defects Research (Part A) 94:S1-S169 (2012)
LouisianaBirth Defects Counts and Prevalence 2005-2008 (Prevalence per 10,000 Live Births)LouisianaBirth Defects Counts and Prevalence 2005-2008 (Prevalence per 10,000 Live Births)
LouisianaBirth Defects Counts and Prevalence 2005-2008 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 34339.2
21230.7
2327.9
928.2
<5.
58834.7
1
Pulmonary valve atresia and stenosis 748.5
547.8
<5.
<5.
00.0
1358.0
Pulmonary valve atresia 131.5
81.2
00.0
00.0
00.0
211.2
Pyloric stenosis 14816.9
426.1
1214.6
<5.
<5.
20712.2
Rectal and large intestinal atresia/stenosis 424.8
253.6
<5.
<5.
<5.
744.4
Reduction deformity, lower limbs 121.4
152.2
<5.
00.0
00.0
291.7
Reduction deformity, upper limbs 192.2
192.7
<5.
00.0
00.0
412.4
Renal agenesis/hypoplasia 475.4
334.8
<5.
00.0
00.0
824.8
Spina bifida without anencephalus 354.0
142.0
<5.
<5.
00.0
533.1
Tetralogy of Fallot 445.0
273.9
<5.
00.0
00.0
744.4
Transposition of great arteries - All 414.7
192.7
<5.
<5.
<5.
633.7
dextro-Transposition of great arteries(d-TGA)
374.2
182.6
<5.
<5.
<5.
583.4
Tricuspid valve atresia and stenosis <5.
111.6
<5.
<5.
00.0
171.0
Tricuspid valve atresia <5.
91.3
<5.
<5.
00.0
150.9
Trisomy 13 (Patau syndrome) <5.
<5.
<5.
00.0
00.0
90.7
Trisomy 18 (Edwards syndrome) 171.9
60.9
<5.
<5.
00.0
271.6
Ventricular septal defect 50557.7
28741.5
3947.4
1546.9
<5.
85250.3
Total Live Births 70886.
54755.
6989.
2525.
588.
136201.
Total Male Live Births 44771.
35126.
4196.
1654.
331.
86377.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S45
Birth Defects Research (Part A) 94:S1-S169 (2012)
LouisianaTrisomy Counts and Prevalence by Maternal Age 2005-2008 (Prevalence per 10,000 Live Births)LouisianaTrisomy Counts and Prevalence by Maternal Age 2005-2008 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 117
7.610162.0
21812.9
Trisomy 13 (Patau syndrome) 70.6
<5.
90.7
Trisomy 18 (Edwards syndrome) 181.2
95.5
271.6
Total Live Births 152990.
16280.
169283.
**Total includes unknown maternal age
Notes1.Includes only if weight =>2500 grams or gestational age >=36 wks, however, unable to define if defect lasted at >= 6 wks of age
General comments-2005-2006 birth data include only live births to Louisiana residents at birth that occurred in regions Greater New Orleans, Baton Rouge, Lake Charlesand Shreveport-2005-2006 birth defects data include only live births to Louisiana residents at birth that occurred in Greater New Orleans, Baton Rouge, Lake Charlesand Shreveport areas.-2007 birth defects data include only live births to Louisiana residents at birth that occurred in Greater New Orleans, Baton Rouge, Lafayette, LakeCharles and Shreveport areas-2007-2009 birth data include only live births to Louisiana residents at birth that occurred in regions Greater New Orleans, Baton Rouge, Lafayette, LakeCharles and Shreveport-2008 birth defects data are provisional and include only live births to Louisiana residents that occurred in Greater New Orleans, Baton Rouge, Lafayette,Lake Charles and Shreveport-2009 birth defects data are not available-All probable cases are included-BPA codes are used to define the birth defects-Hurricane Katrina disrupted the active surveillance in Louisiana and may have created several types of selection bias.-Louisiana is an active surveillance state that began identifying births in 2005. Birth defects surveillance has not been conducted among terminations andstill births yet-The 2009 cohort will not be complete until 12/31/2012 because the LA case definition includes children up to their third birthday.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S46
Birth Defects Research (Part A) 94:S1-S169 (2012)
MaineBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)MaineBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Anencephalus 60.9
00.0
00.0
00.0
00.0
71.0
Cleft lip with and without cleft palate 548.5
00.0
00.0
218.0
117.8
598.7
Cleft palate without cleft lip 548.5
00.0
00.0
00.0
00.0
548.0
Coarctation of aorta 304.7
00.0
00.0
00.0
00.0
304.4
Common truncus 60.9
00.0
00.0
00.0
00.0
60.9
Down syndrome (Trisomy 21) 7612.0
16.2
330.3
00.0
117.8
8612.7
Encephalocele 10.2
00.0
110.1
00.0
00.0
20.3
Gastroschisis 386.0
00.0
00.0
19.0
00.0
395.8
1
Hypoplastic left heart syndrome 193.0
00.0
00.0
00.0
00.0
192.8
Hypospadias* 7358.2
251.9
297.6
143.1
00.0
7857.6
2
Omphalocele 152.4
00.0
00.0
00.0
00.0
162.4
3
Pulmonary valve atresia 30.5
00.0
00.0
00.0
00.0
30.4
Reduction deformity, lower limbs 20.8
00.0
00.0
00.0
00.0
20.8
2
Reduction deformity, upper limbs 20.8
00.0
00.0
00.0
141.5
31.1
2
Spina bifida without anencephalus 223.5
16.2
00.0
00.0
00.0
233.4
Tetralogy of Fallot 213.3
00.0
110.1
00.0
00.0
223.2
4
Transposition of great arteries - All 304.7
16.2
00.0
00.0
117.8
324.7
dextro-Transposition of great arteries(d-TGA)
213.3
16.2
00.0
00.0
00.0
223.2
Tricuspid valve atresia and stenosis 20.3
00.0
00.0
00.0
00.0
20.3
Total Live Births 63264.
1601.
990.
1112.
562.
67735.
Total Male Live Births (2008-2009) 12534.
385.
205.
232.
131.
13536.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S47
Birth Defects Research (Part A) 94:S1-S169 (2012)
MaineTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)MaineTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 46
7.94042.3
8612.7
Total Live Births 58283.
9451.
67735.
**Total includes unknown maternal age
Notes1.Gastroschisis is coded 756.73. Cases are also abstracted to determine diagnosis2.Surveillance for this condition began with 2008 births3.Omphalocele is coded 756.72. Cases are also abstracted to determine diagnosis4.Includes pulmonary atresia with septal defect
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S48
Birth Defects Research (Part A) 94:S1-S169 (2012)
MarylandBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)MarylandBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
MarylandBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia 30.4
10.2
00.0
00.0
00.0
40.3
Pyloric stenosis 20.3
00.0
00.0
00.0
00.0
20.1
Rectal and large intestinal atresia/stenosis 362.0
221.7
61.2
41.6
00.0
681.8
Reduction deformity, lower limbs 352.0
231.8
40.8
10.4
00.0
641.7
Reduction deformity, upper limbs 512.8
342.7
122.4
41.6
00.0
1032.7
Renal agenesis/hypoplasia 603.3
362.8
61.2
62.4
00.0
1112.9
Spina bifida without anencephalus 673.7
272.1
183.6
52.0
00.0
1193.1
Tetralogy of Fallot 201.1
181.4
30.6
52.0
00.0
461.2
Transposition of great arteries - All 261.4
141.1
51.0
52.0
00.0
511.3
dextro-Transposition of great arteries(d-TGA)
70.5
50.5
41.0
10.5
00.0
180.6
Trisomy 13 (Patau syndrome) 231.3
131.0
20.4
31.2
00.0
421.1
Trisomy 18 (Edwards syndrome) 693.8
221.7
153.0
62.4
00.0
1193.1
Ventricular septal defect 392.7
333.2
71.8
105.2
00.0
892.9
2
Total Live Births 179338.
127578.
49402.
25178.
809.
382305.
Total Male Live Births 92040.
64568.
25241.
13105.
.
.195508.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S50
Birth Defects Research (Part A) 94:S1-S169 (2012)
MarylandTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)MarylandTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 203
6.522531.7
42911.2
Trisomy 13 (Patau syndrome) 220.7
202.8
421.1
Trisomy 18 (Edwards syndrome) 491.6
699.7
1193.1
Total Live Births 311626.
70967.
382634.
**Total includes unknown maternal age
Notes1.Weight greater than or equal to 2500 grams2.Includes probable cases
General comments-Critical Congenital Heart Defect - Data is based on hospital reporting and can not be validated through Vital Statistics as there is no requirement tospecify the cardiac defect on the birth certificate.-Hispanic: Includes all births to mothers of Hispanic origin of any race.-The total number of births data was receieved from Vital Statistics-The total number of male live births is not available for American Indian/Alaskan Native category-Total births: Includes races categorized as 'other' .-White(Total), Black, American Indian, Asian or Pacific Islander: Race and Hispanic origin are reported separately on the birth certificate. Data forpersons of Hispanic origin are included in the data for each race group according to the mother' s reported race.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S51
Birth Defects Research (Part A) 94:S1-S169 (2012)
MassachusettsBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)MassachusettsBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
MassachusettsBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Rectal and large intestinal atresia/stenosis 722.8
61.8
203.7
134.6
112.3
1173.0
Reduction deformity, lower limbs 281.1
61.8
142.6
31.1
00.0
521.4
Reduction deformity, upper limbs 632.4
61.8
264.9
51.8
112.3
1042.7
Renal agenesis/hypoplasia 70.3
51.5
20.4
10.4
00.0
170.4
5
Spina bifida without anencephalus 401.5
51.5
112.1
41.4
00.0
641.7
Tetralogy of Fallot 1044.0
216.4
315.8
155.3
00.0
1784.6
Total anomalous pulmonary venous return(TAPVR)
220.8
30.9
40.7
51.8
00.0
340.9
Transposition of great arteries - All 923.5
103.1
132.4
41.4
112.3
1243.2
dextro-Transposition of great arteries(d-TGA)
803.1
72.1
132.4
41.4
112.3
1092.8
Tricuspid valve atresia 170.7
20.6
20.4
00.0
00.0
230.6
Trisomy 13 (Patau syndrome) 190.7
41.2
40.7
00.0
00.0
270.7
Trisomy 18 (Edwards syndrome) 291.1
123.7
132.4
72.5
00.0
631.6
Ventricular septal defect 47618.3
6921.2
10519.6
5619.7
00.0
72718.9
6
Total Live Births 260777.
32623.
53524.
28389.
815.
384688.
Total Male Live Births 133441.
16682.
27423.
14688.
409.
197041.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S53
Birth Defects Research (Part A) 94:S1-S169 (2012)
MassachusettsTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)MassachusettsTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 217
7.327030.4
48712.7
Trisomy 13 (Patau syndrome) 140.5
131.5
270.7
Trisomy 18 (Edwards syndrome) 280.9
353.9
631.6
Total Live Births 295932.
88756.
384688.
**Total includes unknown maternal age
Notes1.Excludes isolated diagnosis without surgical intervention and secondary diagnosis without postnatal confirmation.2.Excludes 1st degree and NOS.3.Defined as head circumference 2 std dev below normal.4.Wt <=2500 gms is excluded. We use a decision tree for coding PDA: never code if on PGE or <36 wks GA. If >=6 weeks code. If <6 wks code iftreated with indocin, ligated or surgically closed or associated with other codable defect.5.Excludes isolated unilateral renal agenesis/hypoplasia.6.Excludes isolated muscular VSDs.
General comments-2009 data are provisional.-Coding system is CDC/BPA.-Differences in numbers from previous publications are the result of updated files.-Possible/probable cases are excluded.-Source for race and Hispanic ethnicity is vital records.-Stillbirths are included, terminations are not included.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S54
Birth Defects Research (Part A) 94:S1-S169 (2012)
MichiganBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)MichiganBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
MichiganBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia and stenosis 46010.6
17816.1
306.6
2713.3
413.1
73211.8
Pulmonary valve atresia 932.1
393.5
92.0
62.9
26.5
1612.6
Pyloric stenosis 84319.4
938.4
6514.3
167.9
516.3
106517.2
Rectal and large intestinal atresia/stenosis 2104.8
484.3
143.1
125.9
26.5
3155.1
Reduction deformity, lower limbs 831.9
292.6
71.5
10.5
26.5
1282.1
Reduction deformity, upper limbs 1112.6
242.2
92.0
21.0
26.5
1522.5
Renal agenesis/hypoplasia 2335.4
676.1
153.3
146.9
413.1
3505.7
Spina bifida without anencephalus 2355.4
423.8
143.1
167.9
26.5
3395.5
Tetralogy of Fallot 2265.2
736.6
163.5
115.4
13.3
3866.2
Total anomalous pulmonary venous return(TAPVR)
461.1
242.2
40.9
52.5
39.8
941.5
Transposition of great arteries - All 2606.0
585.2
81.8
136.4
516.3
4076.6
dextro-Transposition of great arteries(d-TGA)
1804.1
292.6
30.7
83.9
39.8
2564.1
Tricuspid valve atresia and stenosis 631.4
181.6
20.4
31.5
13.3
981.6
Trisomy 13 (Patau syndrome) 320.7
141.3
51.1
21.0
00.0
560.9
Trisomy 18 (Edwards syndrome) 551.3
242.2
30.7
31.5
00.0
861.4
Ventricular septal defect 191944.1
48644.0
9520.9
8642.2
1136.0
276044.6
2
Total Live Births 435184.
110569.
45356.
20365.
3059.
619332.
Total Male Live Births 223154.
56291.
23221.
10570.
1545.
317259.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S56
Birth Defects Research (Part A) 94:S1-S169 (2012)
MichiganTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)MichiganTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 448
8.333440.7
81513.2
Trisomy 13 (Patau syndrome) 410.8
121.5
560.9
Trisomy 18 (Edwards syndrome) 510.9
344.1
861.4
Total Live Births 537132.
82140.
619332.
**Total includes unknown maternal age
Notes1.ICD-9 coding - 1st available for 2010 data2.Include all reported with this code - may include probable cases
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S57
Birth Defects Research (Part A) 94:S1-S169 (2012)
MinnesotaBirth Defects Counts and Prevalence 2006-2009 (Prevalence per 10,000 Live Births)MinnesotaBirth Defects Counts and Prevalence 2006-2009 (Prevalence per 10,000 Live Births)
MinnesotaBirth Defects Counts and Prevalence 2006-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia 40.8
21.1
10.9
32.6
00.0
101.0
Pyloric stenosis 11321.9
137.4
2017.3
32.6
761.0
16717.2
Rectal and large intestinal atresia/stenosis 152.9
74.0
54.3
21.8
00.0
303.1
Reduction deformity, lower limbs 20.4
42.3
10.9
00.0
00.0
80.8
Reduction deformity, upper limbs 51.0
42.3
21.7
43.5
00.0
161.7
Renal agenesis/hypoplasia 152.9
42.3
76.1
32.6
00.0
343.5
Spina bifida without anencephalus 193.7
31.7
32.6
10.9
18.7
282.9
Tetralogy of Fallot 285.4
74.0
10.9
65.3
00.0
434.4
Transposition of great arteries - All 214.1
74.0
32.6
76.2
00.0
394.0
dextro-Transposition of great arteries(d-TGA)
203.9
74.0
32.6
76.2
00.0
383.9
Tricuspid valve atresia 30.6
31.7
00.0
10.9
00.0
70.7
Trisomy 13 (Patau syndrome) 20.4
42.3
32.6
00.0
00.0
90.9
Trisomy 18 (Edwards syndrome) 112.1
52.9
10.9
21.8
00.0
192.0
Ventricular septal defect 14828.7
7040.0
5345.9
2219.4
652.3
31432.4
Total Live Births 51574.
17508.
11542.
11349.
1147.
96859.
Total Male Live Births 26303.
8919.
5850.
5858.
570.
49385.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S59
Birth Defects Research (Part A) 94:S1-S169 (2012)
MinnesotaTrisomy Counts and Prevalence by Maternal Age 2006-2009 (Prevalence per 10,000 Live Births)MinnesotaTrisomy Counts and Prevalence by Maternal Age 2006-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 37
4.76135.6
14114.6
Trisomy 13 (Patau syndrome) 50.6
31.8
90.9
Trisomy 18 (Edwards syndrome) 81.0
63.5
192.0
Total Live Births 79223.
17135.
96859.
**Total includes unknown maternal age
General comments-All data include confirmed cases only-All data include live births only-Data are for Hennepin and Ramsey Counties only-Minnesota uses BPA codes
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S60
Birth Defects Research (Part A) 94:S1-S169 (2012)
MississippiBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)MississippiBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
MississippiBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Rectal and large intestinal atresia/stenosis 252.2
272.7
22.7
14.3
16.5
572.6
Reduction deformity, lower limbs 111.0
121.2
00.0
00.0
00.0
231.0
Reduction deformity, upper limbs 151.3
90.9
11.4
14.3
00.0
281.3
Renal agenesis/hypoplasia 232.1
222.2
11.4
00.0
00.0
462.1
Spina bifida without anencephalus 393.5
141.4
11.4
14.3
16.5
572.6
Tetralogy of Fallot 565.0
494.9
22.7
28.7
16.5
1115.0
Transposition of great arteries - All 353.1
444.4
22.7
14.3
00.0
833.7
Tricuspid valve atresia and stenosis 171.5
222.2
11.4
14.3
00.0
431.9
Trisomy 13 (Patau syndrome) 60.5
70.7
00.0
14.3
00.0
140.6
Trisomy 18 (Edwards syndrome) 90.8
121.2
11.4
00.0
00.0
231.0
Ventricular septal defect 33229.7
31531.7
2027.4
417.3
1064.8
69631.3
2
Total Live Births 111867.
99477.
7297.
2311.
1543.
222541.
Total Male Live Births 57373.
50705.
3745.
1169.
785.
113802.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S62
Birth Defects Research (Part A) 94:S1-S169 (2012)
MississippiTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)MississippiTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 122
5.95030.1
1727.7
Trisomy 13 (Patau syndrome) 130.6
10.6
140.6
Trisomy 18 (Edwards syndrome) 190.9
42.4
231.0
Total Live Births 205902.
16619.
222541.
**Total includes unknown maternal age
Notes1.Cases with =>2500 grams Birth Weights are included for Patent ductus arteriosus.2.Mississippi does not indicate probable causes
General comments-Mississippi uses the ICD-9 coding system.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S63
Birth Defects Research (Part A) 94:S1-S169 (2012)
MissouriBirth Defects Counts and Prevalence 2005-2007 (Prevalence per 10,000 Live Births)MissouriBirth Defects Counts and Prevalence 2005-2007 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Anencephalus 392.1
51.4
64.4
11.8
00.0
512.1
Anophthalmia/microphthalmia 341.8
113.0
10.7
00.0
00.0
461.9
Atrial septal defect 2011109.0
528145.9
140103.8
65117.5
16140.6
2770114.6
Cleft lip with and without cleft palate 24513.3
185.0
2014.8
610.8
217.6
29312.1
Cleft palate without cleft lip 1437.8
185.0
118.2
00.0
18.8
1737.2
Coarctation of aorta 1588.6
298.0
64.4
11.8
18.8
1968.1
Common truncus 211.1
10.3
00.0
00.0
00.0
220.9
Congenital cataract 693.7
102.8
32.2
11.8
00.0
833.4
Diaphragmatic hernia 975.3
174.7
53.7
47.2
00.0
1245.1
Down syndrome (Trisomy 21) 30416.5
3910.8
3123.0
1527.1
326.4
39216.2
Hydrocephalus without spina bifida 1739.4
5114.1
1511.1
35.4
18.8
24310.1
Hypoplastic left heart syndrome 693.7
113.0
21.5
00.0
00.0
853.5
Microcephalus 1136.1
339.1
85.9
23.6
00.0
1566.5
Obstructive genitourinary defect 44824.3
5314.6
4231.1
1425.3
435.1
56323.3
Patent ductus arteriosus 100954.7
20656.9
6951.2
2545.2
543.9
131654.4
Pyloric stenosis 61133.1
5414.9
3626.7
23.6
435.1
71329.5
Rectal and large intestinal atresia/stenosis 1166.3
154.1
107.4
23.6
18.8
1446.0
Reduction deformity, lower limbs 452.4
71.9
00.0
23.6
00.0
542.2
Reduction deformity, upper limbs 563.0
92.5
10.7
11.8
00.0
672.8
Renal agenesis/hypoplasia 1116.0
92.5
64.4
23.6
217.6
1305.4
Spina bifida without anencephalus 965.2
92.5
53.7
11.8
00.0
1114.6
Tetralogy of Fallot 975.3
185.0
53.7
23.6
00.0
1225.0
Transposition of great arteries - All 1085.9
195.2
10.7
35.4
00.0
1335.5
Trisomy 13 (Patau syndrome) 191.0
61.7
64.4
23.6
00.0
331.4
Trisomy 18 (Edwards syndrome) 362.0
113.0
64.4
11.8
00.0
542.2
Ventricular septal defect 85746.5
16445.3
6246.0
2036.1
326.4
111045.9
Total Live Births 184411.
36197.
13485.
5533.
1138.
241783.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S64
Birth Defects Research (Part A) 94:S1-S169 (2012)
MissouriTrisomy Counts and Prevalence by Maternal Age 2005-2007 (Prevalence per 10,000 Live Births)MissouriTrisomy Counts and Prevalence by Maternal Age 2005-2007 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 245
11.314757.5
39216.2
Trisomy 13 (Patau syndrome) 251.2
83.1
331.4
Trisomy 18 (Edwards syndrome) 291.3
259.8
542.2
Total Live Births 216216.
25548.
241783.
**Total includes unknown maternal age
General comments-Missouri has a passive surveillance system and uses ICD-9 codes to identify birth defect cases.-Our surveillance systems uses information from the following files to ascertain cases: birth certificates, death certificates, fetal death certificates,newborn inpatient abstract system, pediatric in- and outpatient abstracts
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S65
Birth Defects Research (Part A) 94:S1-S169 (2012)
NebraskaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)NebraskaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
NebraskaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia and stenosis 656.2
89.3
62.9
00.0
00.0
815.8
Pulmonary valve atresia 131.2
11.2
41.9
00.0
14.3
191.4
Pyloric stenosis 20119.2
44.7
3014.4
39.7
14.3
24117.2
Rectal and large intestinal atresia/stenosis 646.1
22.3
136.3
412.9
14.3
866.1
Reduction deformity, lower limbs 201.9
22.3
00.0
00.0
00.0
221.6
Reduction deformity, upper limbs 353.3
44.7
83.8
00.0
00.0
483.4
Renal agenesis/hypoplasia 484.6
22.3
94.3
13.2
00.0
624.4
Spina bifida without anencephalus 928.8
1011.6
115.3
13.2
00.0
1148.1
Tetralogy of Fallot 353.3
11.2
62.9
00.0
14.3
443.1
Total anomalous pulmonary venous return(TAPVR)
60.6
00.0
73.4
00.0
00.0
130.9
Transposition of great arteries - All 535.1
22.3
52.4
00.0
00.0
614.4
dextro-Transposition of great arteries(d-TGA)
504.8
11.2
52.4
00.0
00.0
574.1
Tricuspid valve atresia 80.8
11.2
10.5
00.0
14.3
130.9
Trisomy 13 (Patau syndrome) 141.3
22.3
73.4
00.0
00.0
241.7
Trisomy 18 (Edwards syndrome) 272.6
55.8
31.4
00.0
14.3
372.6
Ventricular septal defect 40438.6
2225.6
8339.9
722.5
625.9
53538.2
Total Live Births 104763.
8597.
20794.
3107.
2317.
139995.
Total Male Live Births 53571.
4405.
10712.
1593.
1224.
71711.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S67
Birth Defects Research (Part A) 94:S1-S169 (2012)
NebraskaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)NebraskaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 128
10.88741.2
21515.4
Trisomy 13 (Patau syndrome) 201.7
41.9
241.7
Trisomy 18 (Edwards syndrome) 221.9
157.1
372.6
Total Live Births 118877.
21105.
139995.
**Total includes unknown maternal age
Notes1.Includes probable cases
General comments-2009 data are complete
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S68
Birth Defects Research (Part A) 94:S1-S169 (2012)
NevadaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)NevadaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
NevadaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pyloric stenosis 14717.8
158.8
13017.2
53.3
417.1
32116.4
Rectal and large intestinal atresia/stenosis 232.8
95.3
273.6
74.6
00.0
713.6
Reduction deformity, lower limbs 70.8
42.4
131.7
00.0
00.0
241.2
Reduction deformity, upper limbs 151.8
31.8
162.1
00.0
14.3
351.8
Renal agenesis/hypoplasia 323.9
95.3
212.8
95.9
00.0
753.8
Spina bifida without anencephalus 91.1
52.9
212.8
00.0
00.0
371.9
Tetralogy of Fallot 566.8
116.5
405.3
21.3
14.3
1135.8
Total anomalous pulmonary venous return(TAPVR)
70.8
00.0
91.2
10.7
00.0
170.9
Transposition of great arteries - All 394.7
63.5
344.5
10.7
14.3
854.3
dextro-Transposition of great arteries(d-TGA)
182.2
31.8
131.7
00.0
14.3
381.9
Tricuspid valve atresia and stenosis 81.0
63.5
81.1
10.7
14.3
251.3
Trisomy 13 (Patau syndrome) 40.5
10.6
40.5
00.0
00.0
100.5
Trisomy 18 (Edwards syndrome) 81.0
31.8
162.1
21.3
00.0
291.5
Ventricular septal defect 34541.7
5934.7
38350.8
4529.6
1251.3
86144.1
2
Total Live Births 82731.
17008.
75436.
15205.
2338.
195437.
Total Male Live Births 42714.
8686.
38335.
7825.
1147.
100089.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S70
Birth Defects Research (Part A) 94:S1-S169 (2012)
NevadaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)NevadaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 121
General comments-Data are reported for live births and Nevada resident births only.-Nevada uses ICD-9 Coding system.-Probable/possible diagnoses are excluded.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S71
Birth Defects Research (Part A) 94:S1-S169 (2012)
New HampshireBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)New HampshireBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
New HampshireBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 223.5
327.9
00.0
14.0
00.0
324.6
2
Pulmonary valve atresia and stenosis 314.9
218.6
112.5
14.0
00.0
537.6
Pyloric stenosis 11718.5
00.0
337.5
28.1
00.0
16323.3
Rectal and large intestinal atresia/stenosis 162.5
00.0
225.0
00.0
00.0
233.3
Reduction deformity, lower limbs 30.5
00.0
00.0
00.0
00.0
50.7
Reduction deformity, upper limbs 121.9
00.0
112.5
00.0
00.0
202.9
Renal agenesis/hypoplasia 335.2
00.0
337.5
00.0
00.0
476.7
Spina bifida without anencephalus 71.1
00.0
112.5
00.0
00.0
131.9
Tetralogy of Fallot 142.2
19.3
225.0
28.1
00.0
324.6
Transposition of great arteries - All 71.1
00.0
00.0
00.0
00.0
162.3
Tricuspid valve atresia and stenosis 00.0
00.0
00.0
00.0
00.0
20.3
Trisomy 13 (Patau syndrome) 20.3
00.0
00.0
00.0
00.0
50.7
Trisomy 18 (Edwards syndrome) 60.9
00.0
00.0
00.0
00.0
131.9
Ventricular septal defect 10216.1
218.6
337.5
312.1
00.0
15221.7
3
Total Live Births 63183.
1074.
800.
2473.
126.
70082.
Total Male Live Births 32386.
563.
391.
1262.
54.
35905.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S73
Birth Defects Research (Part A) 94:S1-S169 (2012)
New HampshireTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)New HampshireTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 46
8.02419.3
7510.7
Trisomy 13 (Patau syndrome) 20.3
10.8
50.7
Trisomy 18 (Edwards syndrome) 61.0
75.6
131.9
Total Live Births 57567.
12433.
70082.
**Total includes unknown maternal age
Notes1.ICD-9 code data and active medical record abstraction used for all gastroschisis and omphalocele cases2.Includes weight =>2500 grams only3.Probable cases not included
General comments-Data for all birth conditions includes data ascertained during calendar years 2004 through 2009 for NH resident mothers.-Data for live births was obtained from the New Hampshire Department of State, Division of Vital Records Administration, Web Query Tool. Data mayvary from year to year due to the process of continuing acquisition of birth certificate information, particularly from NH residents that give birth out ofstate.-Data includes live births from birth to age 2 years, stillbirths and terminations.-Data is for confirmed cases only, following medical chart review and use of the NBDPN Guidelines.-For gastroschisis and omphalocele, cases are distinguished using active medical chart review.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S74
Birth Defects Research (Part A) 94:S1-S169 (2012)
New JerseyBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)New JerseyBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
New JerseyBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 177567.5
82898.8
108676.0
33462.2
697.4
407572.4
Pulmonary valve atresia and stenosis 2469.3
11213.4
1208.4
326.0
00.0
5239.3
Pulmonary valve atresia 180.7
131.6
151.0
30.6
00.0
530.9
Pyloric stenosis 49318.7
738.7
27919.5
305.6
00.0
90716.1
Rectal and large intestinal atresia/stenosis 752.9
192.3
584.1
203.7
116.2
1753.1
Reduction deformity, lower limbs 451.7
344.1
322.2
91.7
00.0
1242.2
Reduction deformity, upper limbs 572.2
323.8
523.6
163.0
00.0
1663.0
Renal agenesis/hypoplasia 1405.3
303.6
634.4
132.4
116.2
2544.5
Spina bifida without anencephalus 752.9
172.0
523.6
50.9
116.2
1532.7
Tetralogy of Fallot 783.0
495.8
483.4
173.2
00.0
2013.6
Total anomalous pulmonary venous return(TAPVR)
190.7
101.2
161.1
20.4
00.0
470.8
Transposition of great arteries - All 722.7
344.1
513.6
152.8
00.0
1803.2
dextro-Transposition of great arteries(d-TGA)
491.9
121.4
292.0
101.9
00.0
1041.8
Tricuspid valve atresia and stenosis 180.7
161.9
181.3
30.6
00.0
561.0
Trisomy 13 (Patau syndrome) 80.3
20.2
70.5
10.2
00.0
190.3
Trisomy 18 (Edwards syndrome) 230.9
141.7
161.1
50.9
00.0
581.0
Ventricular septal defect 169464.4
48157.4
94265.9
26849.9
464.9
343361.0
4
Total Live Births 263116.
83832.
142918.
53714.
616.
562582.
Total Male Live Births 134977.
42766.
72928.
27450.
327.
287933.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S76
Birth Defects Research (Part A) 94:S1-S169 (2012)
New JerseyTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)New JerseyTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 285
General comments-Hybrid system; passive with audit, uses ICD9-CM codes-Live births only
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S77
Birth Defects Research (Part A) 94:S1-S169 (2012)
New YorkBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)New YorkBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
New YorkBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 170828.5
95947.5
66523.0
29227.2
1460.7
371130.4
Pulmonary valve atresia and stenosis 5038.4
24111.9
2378.2
857.9
313.0
10918.9
Pulmonary valve atresia 400.7
170.8
301.0
40.4
00.0
920.8
Pyloric stenosis 156326.1
26413.1
83328.8
12311.4
1043.3
282523.1
Rectal and large intestinal atresia/stenosis 2514.2
743.7
1394.8
323.0
14.3
5094.2
Reduction deformity, lower limbs 520.9
231.1
150.5
100.9
14.3
1040.9
Reduction deformity, upper limbs 1492.5
371.8
531.8
100.9
14.3
2542.1
Renal agenesis/hypoplasia 3055.1
904.5
1053.6
262.4
28.7
5414.4
Spina bifida without anencephalus 1342.2
462.3
632.2
212.0
14.3
2692.2
Tetralogy of Fallot 2824.7
1185.8
1043.6
615.7
14.3
5794.7
Total anomalous pulmonary venous return(TAPVR)
470.8
180.9
401.4
111.0
00.0
1181.0
Transposition of great arteries - All 1853.1
482.4
682.4
201.9
00.0
3282.7
dextro-Transposition of great arteries(d-TGA)
1752.9
482.4
682.4
181.7
00.0
3162.6
Tricuspid valve atresia and stenosis 621.0
422.1
441.5
171.6
00.0
1681.4
Tricuspid valve atresia 350.6
180.9
190.7
70.7
00.0
800.7
Trisomy 13 (Patau syndrome) 500.8
201.0
281.0
60.6
00.0
1040.9
Trisomy 18 (Edwards syndrome) 581.0
381.9
381.3
60.6
00.0
1451.2
Ventricular septal defect 279046.6
83741.5
132945.9
40337.5
1252.0
547044.8
Total Live Births 598723.
201832.
289265.
107492.
2307.
1221543.
Total Male Live Births 307169.
102881.
147869.
55574.
1124.
625949.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S79
Birth Defects Research (Part A) 94:S1-S169 (2012)
New YorkTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)New YorkTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 696
7.180233.3
149812.3
Trisomy 13 (Patau syndrome) 720.7
321.3
1040.9
Trisomy 18 (Edwards syndrome) 630.6
823.4
1451.2
Total Live Births 980378.
240937.
1221543.
**Total includes unknown maternal age
General comments-2009 data are provisional-NY only ascertains birth defects among live births
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S80
Birth Defects Research (Part A) 94:S1-S169 (2012)
North CarolinaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)North CarolinaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
North CarolinaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia 421.2
342.3
191.8
42.1
11.1
1001.6
Pyloric stenosis 72020.2
966.4
18117.5
105.2
2933.0
103716.2
Rectal and large intestinal atresia/stenosis 1504.2
533.5
525.0
52.6
55.7
2664.2
Reduction deformity, lower limbs 531.5
332.2
212.0
21.0
55.7
1151.8
Reduction deformity, upper limbs 1223.4
583.9
383.7
31.6
66.8
2283.6
Renal agenesis/hypoplasia 2366.6
1046.9
696.7
105.2
78.0
4296.7
Spina bifida without anencephalus 1534.3
402.7
555.3
94.7
22.3
2624.1
Tetralogy of Fallot 1383.9
704.7
302.9
94.7
78.0
2564.0
Total anomalous pulmonary venous return(TAPVR)
361.0
161.1
222.1
52.6
22.3
811.3
Transposition of great arteries - All 1113.1
362.4
323.1
52.6
33.4
1872.9
dextro-Transposition of great arteries(d-TGA)
962.7
332.2
262.5
31.6
22.3
1602.5
Tricuspid valve atresia and stenosis 631.8
392.6
201.9
10.5
33.4
1262.0
Tricuspid valve atresia 521.5
372.5
171.6
10.5
22.3
1091.7
Trisomy 13 (Patau syndrome) 381.1
231.5
151.4
21.0
11.1
801.3
Trisomy 18 (Edwards syndrome) 932.6
372.5
262.5
105.2
22.3
1712.7
Ventricular septal defect 142139.9
59539.8
52550.7
5830.2
4146.6
264541.4
Total Live Births 356226.
149674.
103644.
19192.
8794.
639115.
Total Male Live Births 182972.
76191.
53034.
9952.
4467.
327419.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S82
Birth Defects Research (Part A) 94:S1-S169 (2012)
North CarolinaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)North CarolinaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 451
8.132039.6
77412.1
Trisomy 13 (Patau syndrome) 571.0
232.8
801.3
Trisomy 18 (Edwards syndrome) 981.8
718.8
1712.7
Total Live Births 558240.
80843.
639115.
**Total includes unknown maternal age
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S83
Birth Defects Research (Part A) 94:S1-S169 (2012)
North DakotaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)North DakotaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
North DakotaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pyloric stenosis 7621.4
344.4
00.0
00.0
2041.1
9922.6
Rectal and large intestinal atresia/stenosis 164.5
114.8
00.0
00.0
48.2
214.8
Reduction deformity, lower limbs 41.1
00.0
00.0
00.0
24.1
61.4
Reduction deformity, upper limbs 20.6
00.0
00.0
00.0
12.1
30.7
Renal agenesis/hypoplasia 133.7
00.0
00.0
00.0
48.2
173.9
Spina bifida without anencephalus 215.9
00.0
00.0
00.0
612.3
276.2
Tetralogy of Fallot 174.8
00.0
00.0
00.0
714.4
245.5
Total anomalous pulmonary venous return(TAPVR)
00.0
00.0
00.0
00.0
12.1
10.2
Transposition of great arteries - All 174.8
00.0
00.0
00.0
00.0
173.9
dextro-Transposition of great arteries(d-TGA)
92.5
00.0
00.0
00.0
00.0
92.1
Tricuspid valve atresia and stenosis 51.4
00.0
00.0
00.0
00.0
51.1
4
Tricuspid valve atresia 51.4
00.0
00.0
00.0
00.0
51.1
Trisomy 13 (Patau syndrome) 22.9
178.7
00.0
00.0
00.0
33.6
5
Trisomy 18 (Edwards syndrome) 30.8
00.0
00.0
00.0
12.1
40.9
6
Ventricular septal defect 13136.9
229.6
00.0
00.0
3878.1
17740.5
7
Total Live Births 35465.
675.
1606.
566.
4866.
43716.
Total Male Live Births 18102.
358.
678.
167.
2678.
22249.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S85
Birth Defects Research (Part A) 94:S1-S169 (2012)
North DakotaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)North DakotaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 25
6.41022.4
358.0
Trisomy 13 (Patau syndrome) 22.7
111.8
33.6
5
Trisomy 18 (Edwards syndrome) 30.8
12.2
40.9
6
Total Live Births 39247.
4469.
43716.
**Total includes unknown maternal age
Notes1.State uses ICD-9 code 745.60. .61, .69 for confirmed diagnosis.We cannot distinguish 745.487 CDC/BPA codes.2.The state uses ICD-9 codes and cannot distinguish these two conditions (Epispadias, Hypospadias) often unless reported.3.Infants< 2500 grams are unable to be excluded.4.State uses ICD-9 code 746.1 for confirmed diagnosis.We cannot distinguish 746.105 and 746.106 CDC/BPA codes.5.Trisomy 13 was collected in the birth certificates up to the year 2005. Data for Trisomy 13 are for the year 2005 only. Trisomy 13 is not being colletedin the new electronic birth certificates from the year 2006 onwards.6.Trisomy 18 was collected in the birth certificates up to the year 2005. Data for Trisomy 18 are for the years 2005 through 2009. Trisomy 18 is notbeing collected in the new electronic birth certificates from the year 2006 onwards.7.State uses ICD-9 code 745.4 for confirmed diagnosis.We cannot distinguish 745.487 and 745.498 CDC/BPA codes.
General comments-Fetal Death or birth resulting in stillbirth means death prior to the complete expulsion or extraction from its mother of a product of human conception,irrespective of the duration of pregnancy. The death is indicated by the fact that after such expulsion or extraction the fetus does not breathe or show anyevidence of life such as beating of the heart, pulsation of the umbilical cord, or definite movement of voluntary muscles. North Dakota does not requirereporting of this event before 20 weeks of gestation. Although collection is attempted, reporting is poor.-North Dakota Vital Statistics implemented electronic registration of births from 2006 onwards.-The North Dakota Birth Defects Monitoring System master registry is translated to ICD-9 using ICD-10 codes from birth certificates.-There was no major methodological changes in the registry for the year 2011.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S86
Birth Defects Research (Part A) 94:S1-S169 (2012)
OhioBirth Defects Counts and Prevalence 2008 (Prevalence per 10,000 Live Births)OhioBirth Defects Counts and Prevalence 2008 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
American Indianor AlaskanNative Total** Notes
Cleft lip with and without cleftpalate
11910.5
145.6
57.3
39.6
00.0
1419.5
1
Cleft palate without cleft lip 948.3
197.7
34.4
26.4
00.0
1187.9
2
Spina bifida withoutanencephalus
393.4
31.2
34.4
00.0
00.0
453.0
3
Total Live Births 113542.
24818.
6887.
3129.
216.
148592.
**Total includes unknown race
Notes1.Cleft lip with and without cleft palate: Data pulled on 14JUL2011.2.Cleft palate without cleft lip: Includes one late reported case after lock-down of birth records. Data pulled on 14JUL2011.3.Spina bifida: Livebirths only. Includes one late reported case after lock-down of birth records. Data pulled on 05JUL2011.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S87
Birth Defects Research (Part A) 94:S1-S169 (2012)
OklahomaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)OklahomaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
OklahomaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 00.0
00.0
00.0
00.0
00.0
00.0
Pulmonary valve atresia and stenosis 1167.9
188.7
174.9
24.1
207.8
1746.5
Pulmonary valve atresia 161.1
41.9
41.2
12.1
31.2
281.0
Pyloric stenosis 76952.2
4019.3
10831.1
612.4
14657.3
107440.0
Rectal and large intestinal atresia/stenosis 1228.3
199.2
154.3
24.1
176.7
1756.5
Reduction deformity, lower limbs 46431.5
5828.1
8223.6
918.5
6023.5
67625.2
Reduction deformity, upper limbs 714.8
115.3
82.3
12.1
145.5
1063.9
Renal agenesis/hypoplasia 1107.5
136.3
164.6
36.2
114.3
1555.8
Spina bifida without anencephalus 916.2
83.9
61.7
00.0
103.9
1164.3
Tetralogy of Fallot 765.2
146.8
144.0
00.0
176.7
1214.5
Total anomalous pulmonary venous return(TAPVR)
261.8
52.4
72.0
00.0
83.1
461.7
Transposition of great arteries - All 513.5
41.9
72.0
24.1
103.9
742.8
dextro-Transposition of great arteries(d-TGA)
453.1
41.9
61.7
24.1
103.9
672.5
Tricuspid valve atresia and stenosis 191.3
41.9
41.2
00.0
10.4
281.0
Tricuspid valve atresia 161.1
41.9
30.9
00.0
10.4
240.9
Trisomy 13 (Patau syndrome) 201.4
41.9
00.0
12.1
72.7
321.2
Trisomy 18 (Edwards syndrome) 402.7
83.9
20.6
12.1
52.0
562.1
Ventricular septal defect 94764.3
13665.8
16547.5
2449.4
15661.2
143253.3
Total Live Births 147354.
20674.
34758.
4854.
25480.
268661.
Total Male Live Births 75408.
10600.
17732.
2484.
12969.
137407.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S89
Birth Defects Research (Part A) 94:S1-S169 (2012)
OklahomaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)OklahomaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 175
7.114464.6
31911.9
Trisomy 13 (Patau syndrome) 251.0
73.1
321.2
Trisomy 18 (Edwards syndrome) 391.6
177.6
562.1
Total Live Births 246360.
22283.
268661.
**Total includes unknown maternal age
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S90
Birth Defects Research (Part A) 94:S1-S169 (2012)
Puerto RicoBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)Puerto RicoBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Puerto RicoBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Ventricular septal defect ..
.
.56023.7
.
...
56023.7
11
Total Live Births ..
.
.236699.
.
...
236699.
Total Male Live Births (2007-2009) ..
.
.70552.
.
...
70552.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S92
Birth Defects Research (Part A) 94:S1-S169 (2012)
Puerto RicoTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)Puerto RicoTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 209
9.614674.7
35515.0
Trisomy 13 (Patau syndrome) 271.2
126.1
391.6
Trisomy 18 (Edwards syndrome) 542.5
3618.4
903.8
Total Live Births 217092.
19545.
236699.
**Total includes unknown maternal age
Notes1.Anophtalmia/microphtalmia: Only include data for 2008-2009.2.Anotia/microtia: Only include data for 2008-20093.Excludes PFO4.Only includes AV Canal.5.Bladder exstrophy: Only include data for 2008-20096.Epispadias: Only include data for 2007-20097.We used clinical diagnosis to distinguish gastroschisis and omphalocele.8.Hypospadias: Only include data for 2007-20099.Unable to exclude infants with defect last noted at <6 wks of age.10.Excludes 745.11 (DORV)11.Excludes probable cases. We can't distinguish inlet VSD from other VSD. However we exclude inlet/posterior type VSD in the presence of AV Canal.
General comments-Probable/possible diagnoses were not included.-The coding system used was ICD 9 CM-We include stillbirths and terminations (no gestational age cut off) in our counts.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S93
Birth Defects Research (Part A) 94:S1-S169 (2012)
Rhode IslandBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)Rhode IslandBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Rhode IslandBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 13636.1
2549.6
4938.7
725.9
117.7
21936.1
Pulmonary valve atresia and stenosis 287.4
24.0
1310.3
27.4
117.7
498.1
Pulmonary valve atresia 51.3
00.0
21.6
00.0
117.7
81.3
Pyloric stenosis 20.5
00.0
10.8
00.0
00.0
30.5
Rectal and large intestinal atresia/stenosis 133.5
47.9
43.2
13.7
00.0
223.6
Reduction deformity, lower limbs 71.9
00.0
21.6
00.0
00.0
91.5
Reduction deformity, upper limbs 61.6
12.0
10.8
00.0
00.0
81.3
Renal agenesis/hypoplasia 41.1
36.0
10.8
00.0
00.0
81.3
Spina bifida without anencephalus 82.1
24.0
54.0
00.0
00.0
152.5
Tetralogy of Fallot 133.5
36.0
86.3
00.0
00.0
264.3
Total anomalous pulmonary venous return(TAPVR)
20.5
00.0
32.4
00.0
00.0
50.8
Transposition of great arteries - All 71.9
12.0
43.2
27.4
00.0
142.3
dextro-Transposition of great arteries(d-TGA)
51.3
12.0
43.2
13.7
00.0
111.8
Tricuspid valve atresia 10.3
12.0
10.8
00.0
117.7
40.7
Trisomy 13 (Patau syndrome) 00.0
24.0
21.6
13.7
00.0
61.0
Trisomy 18 (Edwards syndrome) 71.9
24.0
21.6
00.0
00.0
122.0
Ventricular septal defect 14137.5
1427.8
4233.2
1244.4
117.7
21535.4
Total Live Births 37623.
5036.
12652.
2703.
565.
60715.
Total Male Live Births 19460.
2579.
6367.
1361.
286.
31137.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S95
Birth Defects Research (Part A) 94:S1-S169 (2012)
Rhode IslandTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)Rhode IslandTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 38
7.64137.9
8313.7
Trisomy 13 (Patau syndrome) 20.4
43.7
61.0
Trisomy 18 (Edwards syndrome) 51.0
76.5
122.0
Total Live Births 49906.
10809.
60715.
**Total includes unknown maternal age
General comments-Includes specialty clinic data from 2009-Prenatal ascertainment of cases begins in 2009
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S96
Birth Defects Research (Part A) 94:S1-S169 (2012)
South CarolinaBirth Defects Counts and Prevalence 2006-2009 (Prevalence per 10,000 Live Births)South CarolinaBirth Defects Counts and Prevalence 2006-2009 (Prevalence per 10,000 Live Births)
South CarolinaBirth Defects Counts and Prevalence 2006-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Rectal and large intestinal atresia/stenosis 241.8
91.1
20.8
12.5
110.0
371.5
Reduction deformity, lower limbs 251.8
162.0
52.1
00.0
00.0
461.9
Reduction deformity, upper limbs 292.1
192.3
125.0
00.0
110.0
612.5
Renal agenesis/hypoplasia 342.5
202.5
62.5
00.0
00.0
602.4
Spina bifida without anencephalus 493.6
172.1
62.5
12.5
00.0
732.9
Tetralogy of Fallot 453.3
394.8
125.0
12.5
00.0
994.0
Transposition of great arteries - All 664.8
283.4
83.3
12.5
110.0
1064.3
dextro-Transposition of great arteries(d-TGA)
392.8
111.4
31.2
00.0
110.0
552.2
Tricuspid valve atresia and stenosis 80.6
81.0
52.1
00.0
00.0
210.8
Trisomy 13 (Patau syndrome) 71.0
61.5
10.8
00.0
00.0
151.2
5
Trisomy 18 (Edwards syndrome) 152.2
82.0
43.4
00.0
00.0
272.2
6
Ventricular septal defect 42030.7
25130.8
12150.4
922.5
220.0
81132.7
Total Live Births 136903.
81439.
24022.
3998.
999.
250776.
**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S98
Birth Defects Research (Part A) 94:S1-S169 (2012)
South CarolinaTrisomy Counts and Prevalence by Maternal Age 2006-2009 (Prevalence per 10,000 Live Births)South CarolinaTrisomy Counts and Prevalence by Maternal Age 2006-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 64
5.86044.6
1249.9
2
Trisomy 13 (Patau syndrome) 121.1
32.2
151.2
5
Trisomy 18 (Edwards syndrome) 171.5
107.4
272.2
6
Total Live Births 111204.
13447.
124654.
**Total includes unknown maternal age
Notes1.Atrial Septal Defect was dropped beginning in 20092.Down Syndrome was collected beginning in 20083.Patent Ductus Arteriosus was dropped beginning in 20094.Pyloric Stenosis was dropped beginning in 20095.Trisomy 13 was collected beginning in 20086.Trisomy 18 was collected beginning in 2008
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S99
Birth Defects Research (Part A) 94:S1-S169 (2012)
TennesseeBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)TennesseeBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S100
Birth Defects Research (Part A) 94:S1-S169 (2012)
TennesseeBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia and stenosis 30710.8
10311.8
297.5
56.2
232.1
44710.6
Pulmonary valve atresia 441.5
172.0
82.1
00.0
00.0
701.7
Pyloric stenosis 140149.4
23026.4
18347.4
1012.4
116.0
182943.5
Rectal and large intestinal atresia/stenosis 1716.0
475.4
246.2
33.7
00.0
2475.9
Reduction deformity, lower limbs 531.9
252.9
71.8
22.5
00.0
882.1
Reduction deformity, upper limbs 562.0
202.3
123.1
22.5
00.0
912.2
Renal agenesis/hypoplasia 1404.9
515.9
194.9
45.0
00.0
2145.1
Spina bifida without anencephalus 1214.3
293.3
297.5
11.2
00.0
1814.3
Tetralogy of Fallot 1776.2
526.0
194.9
56.2
00.0
2536.0
Transposition of great arteries - All 1826.4
546.2
246.2
45.0
00.0
2656.3
5
dextro-Transposition of great arteries(d-TGA)
672.4
192.2
82.1
33.7
00.0
972.3
Tricuspid valve atresia and stenosis 401.4
70.8
10.3
00.0
00.0
491.2
6
Tricuspid valve atresia 401.4
70.8
10.3
00.0
00.0
491.2
6
Trisomy 13 (Patau syndrome) 170.6
131.5
30.8
11.2
00.0
340.8
Trisomy 18 (Edwards syndrome) 461.6
131.5
92.3
00.0
00.0
681.6
Ventricular septal defect 134147.2
38644.4
18247.1
2126.1
116.0
193746.1
7
Total Live Births 283873.
86969.
38615.
8043.
624.
420278.
Total Male Live Births 145385.
44223.
19659.
4131.
313.
214748.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S101
Birth Defects Research (Part A) 94:S1-S169 (2012)
TennesseeTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)TennesseeTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 355
9.425058.6
60514.4
Trisomy 13 (Patau syndrome) 250.7
92.1
340.8
Trisomy 18 (Edwards syndrome) 461.2
225.2
681.6
Total Live Births 377393.
42668.
420278.
**Total includes unknown maternal age
Notes1.TN does not use the new CDC/BPA codes and cannot distinguish 745.487 from other VSD.2.ICD-9 Procedure Code = 54.713.ICD-9 Procedure Code not equal to 54.714.Birthweight = 2500 grams.5.TN does not use the new CDC/BPA codes: information includes the entire range.6.TN does not use the new CDC/BPA codes and cases with 746.106 are included within this category7.Includes probable cases. TN does not use the new CDC/BPA codes and cannot distinguish 745.487.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S102
Birth Defects Research (Part A) 94:S1-S169 (2012)
TexasBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)TexasBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S103
Birth Defects Research (Part A) 94:S1-S169 (2012)
TexasBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Patent ductus arteriosus 370253.8
121153.6
612961.4
35348.7
1644.5
1147857.4
1
Pulmonary valve atresia and stenosis 6249.1
24110.7
106610.7
415.7
513.9
19849.9
Pulmonary valve atresia 871.3
311.4
1631.6
60.8
00.0
2891.4
2
Pyloric stenosis 152222.1
1948.6
216721.7
314.3
616.7
393219.7
Rectal and large intestinal atresia/stenosis 3685.3
994.4
5645.7
324.4
38.3
10785.4
Reduction deformity, lower limbs 1512.2
622.7
1781.8
81.1
00.0
4012.0
Reduction deformity, upper limbs 3044.4
974.3
3933.9
192.6
719.4
8224.1
Renal agenesis/hypoplasia 3965.8
1275.6
6146.2
283.9
411.1
11765.9
Spina bifida without anencephalus 2383.5
572.5
4154.2
81.1
25.6
7263.6
Tetralogy of Fallot 2734.0
1094.8
3623.6
354.8
38.3
7924.0
Total anomalous pulmonary venous return(TAPVR)
931.4
200.9
2292.3
101.4
12.8
3551.8
Transposition of great arteries - All 2693.9
632.8
3523.5
273.7
25.6
7143.6
3
dextro-Transposition of great arteries(d-TGA)
2563.7
642.8
3533.5
263.6
25.6
7033.5
4
Tricuspid valve atresia and stenosis 1091.6
492.2
1921.9
141.9
00.0
3671.8
Tricuspid valve atresia 500.7
221.0
750.8
71.0
00.0
1550.8
Trisomy 13 (Patau syndrome) 751.1
291.3
1091.1
101.4
00.0
2251.1
Trisomy 18 (Edwards syndrome) 1862.7
662.9
2602.6
233.2
12.8
5442.7
Ventricular septal defect 390656.7
106547.2
689969.1
33846.6
1952.8
1228961.5
5
Total Live Births 688672.
225737.
997993.
72455.
3599.
1999140.
Total Male Live Births 353805.
114886.
508998.
37139.
1868.
1022134.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S104
Birth Defects Research (Part A) 94:S1-S169 (2012)
TexasTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)TexasTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 1521
8.6117050.5
269113.5
Trisomy 13 (Patau syndrome) 1600.9
652.8
2251.1
Trisomy 18 (Edwards syndrome) 2981.7
24610.6
5442.7
Total Live Births 1767472.
231538.
1999140.
**Total includes unknown maternal age
Notes1.Patent ductus arteriosus: In Texas, coding of patent ductus arteriosus (PDA) is based on the following criteria. PDA is never coded if the infant wasless than 36 weeks gestation and less than 12 weeks of age at diagnosis, or if the infant was on prostaglandin. If the infant was greater than or equal to 36weeks gestation and less than 12 weeks of age at diagnosis, PDA is coded only if there is another reportable defect present, or if there was amedical/surgical intervention for this problem. PDA is always coded if the infant is greater than or equal to 12 weeks of age at diagnosis, unless the infantwas on prostaglandin.2.Pulmonary valve atresia for CCHD: Excludes TOF.3.Transposition of the great arteries: As Texas does not use the new CDC BPA codes and the exclusion criteria has '745.180', those defects of 'doubleoutlet right ventricle' which we have coded into 745.180 will not be counted in this defect.4.Transposition of the great arteries for CCHD: Data are provisional.5.Ventricular Septal Defect: We are unable to distinguish inlet VSD from other types of VSD.
General comments-Our case definition includes livebirths, stillbirths, and terminations at any length of gestation and any birthweight.-Texas only reports confirmed and definite diagnoses for any defect reported. Possible/probable cases are not given.-Texas uses the CDC/BPA coding system, but does not use the new CDC/BPA codes.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S105
Birth Defects Research (Part A) 94:S1-S169 (2012)
UtahBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)UtahBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S106
Birth Defects Research (Part A) 94:S1-S169 (2012)
UtahBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pyloric stenosis 31715.1
14.1
8118.8
67.0
411.8
41115.2
Rectal and large intestinal atresia/stenosis 844.0
28.2
204.6
22.3
25.9
1104.1
Reduction deformity, lower limbs 361.7
14.1
61.4
55.8
00.0
481.8
Reduction deformity, upper limbs 1125.3
00.0
307.0
55.8
13.0
1505.6
Renal agenesis/hypoplasia 683.2
28.2
173.9
33.5
00.0
913.4
Spina bifida without anencephalus 934.4
14.1
184.2
11.2
25.9
1154.3
Tetralogy of Fallot 683.2
28.2
163.7
55.8
25.9
943.5
Total anomalous pulmonary venous return(TAPVR)
211.0
00.0
71.6
22.3
25.9
321.2
Transposition of great arteries - All 894.2
28.2
225.1
44.7
13.0
1204.5
dextro-Transposition of great arteries(d-TGA)
502.4
00.0
81.9
22.3
00.0
602.2
Tricuspid valve atresia 221.1
00.0
61.4
33.5
00.0
311.2
Trisomy 13 (Patau syndrome) 361.7
28.2
184.2
11.2
00.0
572.1
Trisomy 18 (Edwards syndrome) 713.4
416.5
163.7
22.3
13.0
963.6
Ventricular septal defect 47022.4
1457.7
11125.7
1820.9
1029.6
62523.2
Total Live Births 209441.
2426.
43141.
8597.
3381.
269509.
Total Male Live Births 107861.
1264.
21890.
4505.
1718.
138538.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S107
Birth Defects Research (Part A) 94:S1-S169 (2012)
UtahTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)UtahTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 223
9.117168.0
39414.6
Trisomy 13 (Patau syndrome) 381.6
197.6
572.1
Trisomy 18 (Edwards syndrome) 572.3
3915.5
963.6
Total Live Births 244335.
25161.
269509.
**Total includes unknown maternal age
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S108
Birth Defects Research (Part A) 94:S1-S169 (2012)
VirginiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)VirginiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S109
Birth Defects Research (Part A) 94:S1-S169 (2012)
VirginiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pulmonary valve atresia and stenosis 2799.1
13712.0
7210.3
5715.8
00.0
66312.5
Pulmonary valve atresia 260.9
161.4
81.1
51.4
00.0
631.2
Pyloric stenosis 52117.1
968.4
7210.3
154.2
339.5
77214.5
Rectal and large intestinal atresia/stenosis 1244.1
332.9
223.1
61.7
00.0
2104.0
Reduction deformity, lower limbs 371.2
171.5
30.4
30.8
113.2
671.3
Reduction deformity, upper limbs 812.7
242.1
121.7
51.4
00.0
1322.5
Renal agenesis/hypoplasia 933.0
282.4
162.3
61.7
00.0
1623.1
Spina bifida without anencephalus 1193.9
453.9
273.8
41.1
00.0
2414.5
Tetralogy of Fallot 1133.7
494.3
233.3
164.4
113.2
2334.4
Transposition of great arteries - All 1645.4
403.5
243.4
143.9
00.0
2885.4
dextro-Transposition of great arteries(d-TGA)
782.6
141.2
101.4
61.7
00.0
1252.4
Tricuspid valve atresia and stenosis 240.8
121.0
40.6
51.4
00.0
551.0
Trisomy 13 (Patau syndrome) 180.6
50.4
91.3
10.3
00.0
400.8
Trisomy 18 (Edwards syndrome) 391.3
131.1
60.9
82.2
00.0
761.4
Ventricular septal defect 137445.0
37833.0
35650.7
17749.0
339.5
268550.6
Total Live Births 305140.
114481.
70231.
36102.
760.
530936.
Total Male Live Births 156663.
57923.
36118.
18518.
359.
271762.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S110
Birth Defects Research (Part A) 94:S1-S169 (2012)
VirginiaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)VirginiaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 312
7.028633.0
68312.9
Trisomy 13 (Patau syndrome) 220.5
111.3
400.8
Trisomy 18 (Edwards syndrome) 350.8
313.6
761.4
Total Live Births 443714.
86753.
530936.
**Total includes unknown maternal age
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S111
Birth Defects Research (Part A) 94:S1-S169 (2012)
West VirginiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)West VirginiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S112
Birth Defects Research (Part A) 94:S1-S169 (2012)
West VirginiaBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pyloric stenosis 707.5
12.8
00.0
00.0
00.0
798.0
Rectal and large intestinal atresia/stenosis 222.4
12.8
18.6
00.0
00.0
272.7
Reduction deformity, lower limbs 80.9
00.0
00.0
00.0
00.0
80.8
Reduction deformity, upper limbs 111.2
12.8
00.0
00.0
00.0
121.2
Renal agenesis/hypoplasia 262.8
00.0
00.0
00.0
00.0
303.0
Spina bifida without anencephalus 333.6
00.0
00.0
00.0
00.0
333.3
Tetralogy of Fallot 283.0
12.8
18.6
00.0
00.0
363.6
Total anomalous pulmonary venous return(TAPVR)
30.3
00.0
00.0
00.0
00.0
60.6
Transposition of great arteries - All 242.6
00.0
00.0
00.0
00.0
323.2
dextro-Transposition of great arteries(d-TGA)
101.1
00.0
00.0
00.0
00.0
151.5
Tricuspid valve atresia and stenosis 70.8
00.0
00.0
00.0
00.0
131.3
Trisomy 13 (Patau syndrome) 60.6
00.0
00.0
00.0
00.0
101.0
Trisomy 18 (Edwards syndrome) 101.1
00.0
00.0
00.0
00.0
111.1
Ventricular septal defect 19420.9
38.5
00.0
111.5
00.0
22722.9
Total Live Births 92855.
3550.
1167.
867.
119.
99295.
Total Male Live Births 46430.
1807.
581.
466.
51.
49662.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S113
Birth Defects Research (Part A) 94:S1-S169 (2012)
West VirginiaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)West VirginiaTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 46
5.01722.5
727.3
Trisomy 13 (Patau syndrome) 80.9
11.3
101.0
Trisomy 18 (Edwards syndrome) 70.8
34.0
111.1
Total Live Births 91735.
7559.
99295.
**Total includes unknown maternal age
Notes1.Includes only births =>2500 grams or =>36 wks gestation.
General comments-Birth defects defined by ICD-9 coding.-No metholologic changes during this period.-Probable cases are included.-Stillbirths and terminations per birth defect are not collected.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S114
Birth Defects Research (Part A) 94:S1-S169 (2012)
WisconsinBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)WisconsinBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S115
Birth Defects Research (Part A) 94:S1-S169 (2012)
WisconsinBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Pyloric stenosis 30.1
00.0
00.0
00.0
00.0
30.1
Rectal and large intestinal atresia/stenosis 863.4
61.7
92.7
32.2
11.9
1053.1
Reduction deformity, lower limbs 291.2
41.1
41.2
21.4
00.0
391.1
Reduction deformity, upper limbs 652.6
102.9
92.7
42.9
35.6
912.7
Renal agenesis/hypoplasia 893.5
61.7
92.7
53.6
11.9
1103.2
Spina bifida without anencephalus 783.1
102.9
92.7
21.4
11.9
1002.9
Tetralogy of Fallot 542.1
133.7
113.3
21.4
11.9
812.4
Total anomalous pulmonary venous return(TAPVR)
40.2
00.0
10.3
00.0
00.0
50.1
Transposition of great arteries - All 461.8
51.4
123.6
10.7
11.9
651.9
dextro-Transposition of great arteries(d-TGA)
331.3
20.6
51.5
10.7
11.9
421.2
Tricuspid valve atresia and stenosis 150.6
41.1
20.6
10.7
00.0
220.6
Tricuspid valve atresia 10.0
00.0
10.3
00.0
00.0
20.1
Trisomy 13 (Patau syndrome) 200.8
20.6
30.9
10.7
00.0
260.8
Trisomy 18 (Edwards syndrome) 572.3
61.7
72.1
10.7
00.0
722.1
Ventricular septal defect 62724.9
5616.1
11534.5
3525.2
2139.1
85425.2
1
Total Live Births 251798.
34819.
33317.
13874.
5373.
339341.
Total Male Live Births 129258.
17551.
16984.
7062.
2708.
173652.
*Hypospadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S116
Birth Defects Research (Part A) 94:S1-S169 (2012)
WisconsinTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)WisconsinTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 220
7.520646.6
42612.6
Trisomy 13 (Patau syndrome) 170.6
40.9
210.6
Trisomy 18 (Edwards syndrome) 230.8
163.6
391.1
Total Live Births 295093.
44200.
339341.
**Total includes unknown maternal age
Notes1.Hospital practice in coding is not known.
General comments-Anencephaly, Spina Bifida, Down Syndrome, Trisomy 13, and Trisomy 18 data include livebirths and stillbirths (although trisomy data in the maternal agetable include only livebirths). Data for all other defects include only livebirths.-As in the past, Wisconsin used its linked birth-hospital discharge records. Live births that were not linked to a newborn discharge record are notincluded. Since the discharge records are only available from Wisconsin hospitals, only Wisconsin resident births occurring in Wisconsin hospitals areincluded.-Questions? [email protected] discharge records include a primary diagnosis and up to eight other diagnoses; all were scanned for the conditions. The diagnoses are ICD-9 coded.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S117
Birth Defects Research (Part A) 94:S1-S169 (2012)
Department of DefenseBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)Department of DefenseBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S118
Birth Defects Research (Part A) 94:S1-S169 (2012)
Department of DefenseBirth Defects Counts and Prevalence 2005-2009 (Prevalence per 10,000 Live Births)
Maternal Race/Ethnicity
DefectNon-Hispanic White
Non-Hispanic Blackor African Hispanic
Asian or PacificIslander
AmericanIndian orAlaskan Native Total** Notes
Rectal and large intestinal atresia/stenosis 2206.1
364.5
243.9
208.1
33.0
3095.6
Reduction deformity, lower limbs 922.5
243.0
91.5
41.6
44.0
1362.5
Reduction deformity, upper limbs 1163.2
162.0
213.4
83.3
22.0
1643.0
Renal agenesis/hypoplasia 2065.7
202.5
335.4
114.5
65.9
2825.1
Spina bifida without anencephalus 1815.0
243.0
264.2
83.3
65.9
2544.6
1
Tetralogy of Fallot 2236.2
485.9
365.9
239.4
98.9
3456.3
Total anomalous pulmonary venous return(TAPVR)
501.4
131.6
132.1
52.0
00.0
851.5
Transposition of great arteries - All 2125.9
374.6
376.0
176.9
33.0
3105.6
dextro-Transposition of great arteries(d-TGA)
1383.8
232.8
193.1
145.7
22.0
1993.6
Tricuspid valve atresia and stenosis 541.5
151.9
30.5
10.4
11.0
761.4
Trisomy 13 (Patau syndrome) 481.3
172.1
71.1
10.4
00.0
751.4
1
Trisomy 18 (Edwards syndrome) 681.9
111.4
132.1
52.0
00.0
981.8
1
Ventricular septal defect 268074.2
47558.8
43270.3
14960.7
7170.2
388270.5
4
Total Live Births 361422.
80801.
61447.
24552.
10116.
550562.
Total Male Live Births 186253.
41071.
31446.
12636.
5184.
282914.
*Hypospadias and Epispadias: prevalence per 10,000 male live births**Total includes unknown race
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S119
Birth Defects Research (Part A) 94:S1-S169 (2012)
Department of DefenseTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)Department of DefenseTrisomy Counts and Prevalence by Maternal Age 2005-2009 (Prevalence per 10,000 Live Births)
Age
Defect Less than 35 35 and greater Total** NotesDown syndrome (Trisomy 21) 505
10.525450.7
78614.3
1
Trisomy 13 (Patau syndrome) 581.2
153.0
751.4
1
Trisomy 18 (Edwards syndrome) 581.2
367.2
981.8
1
Total Live Births 480438.
50143.
550562.
**Total includes unknown maternal age
Notes1.DoD Registry only captures livebirths2.DoD Registry relies on ICD-9-CM codes and cannot differentiate PFO3.DoD Registry relies on ICD-9-CM codes and cannot distinguish 745.4874.All ICD-9-CM coded cases that meet DoD Registry case criteria are included. DoD Registry relies on ICD-9-CM codes and cannot distinguish745.487
General comments-Criteria for a case: One diagnosis from institutional records, or 2 diagnoses from professional encounter records-Infants that appear as multiples of same gender are excluded from analysis-Race/Ethnicity for the DoD Birth and Infant Health Registry is based on the military parent through whom the infant receives military health carebenefits. This may be the infants' mother or father.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S120
Birth Defects Research (Part A) 94:S1-S169 (2012)
STATE BIRTH DEFECTS SURVEILLANCE
PROGRAM DIRECTORY
Updated September 2012
Prepared by the National Center on Birth Defects and Developmental Disabilities, Centers for Disease
Control and Prevention
Acknowledgement: State birth defects program directors provided the information for the directory.
Their names can be found under the “contact” section of each state profile.
STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DIRECTORY S121