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    MUHIMBILI UNIVERSITY OFHEALTH AND ALLIED

    SCIENCES.

    SCHOOL OF NURSING.DERPARTMENT OF CLINICAL NURSINGPEDIATRIC NURSING( PD300)

    PRESENTATION:TOPIC - TRACHEOESOPHAGEAL FISTULA

    PRESENTER:JOHN, So !o"# .R$! NO %00&-0'-0 ' *

    SUPERVISOR :MR. MENTI NDILE

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    INTRODUCTION• E+o #!$# #/ $+1# (EA) 1+ / $ 2o !$ 1/#

    "# o "#/1o / #/ $ $+$ / / $ #1 4 $ o / $$+o #!4+ /o 5$6$ o # 2o /1 4o4+ #++#!$ 4 /o/ $ +/o"#2

    T#2 $o $+o #!$# 7+/4 # (TEF) 1+ / $ 2o !$ 1/#"# o "#/1o 8 $ $ / $ / #2 $# # 5 $+o #!4+#1 + /o +$ # #/$ 1 /o 51+/1 2/ +/ 42/4 $+ # 5 ##++#!$ 1+ 2 $#/$5 9$/8$$ / $ /8o.

    • T#2 $o$+o #!$# 5$ $2/ 1+ # +$ 1o4+, 2o !$ 1/#2o 51/1o 1 8 12 / $ $ 1+ # #9 o "#2o $2/1o 9$/8$$ / $ / #2 $# # 5 / $$+o #!4+ / $ $+o #!4+ $ 5+ 9$ o $ $#2 1 !/ $ +/o"#2 # 5;o / $ $+o #!4+ 5$6$ o + #+ #o42 2o $2/$5 /o / $ / #2 $# 9< # 7+/4 # .

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    E+o #!4+ : /49$ / #/ 2o $2/+ / $"o4/ /o / $ +/o"#2

    T #2 $#: =81 5 1 $> A/ $+1# : #9+$ 2$ o # o "# o $ 1 !

    Co !$ 1/# : o4 5 #/ 91 / . F1+/4 # : #9 o "# #++#!$ o" # 9o5<

    o !# /o / $ 9o5< +4 #2$ o 9$/8$$/8o 1 /$ # 9o5< o !# +.

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    CLASSIFICATION OF TEF@ C #++17$5 9< A"$ 12# A2#5$"< o P$51#/ 12+ #+• TYPE A : I/ 2o +1+/+ o 9 1 5 4 $ # 5 9 1 5 o8$

    $+o #!$# +$!"$ / 81/ o4/ # < / #2 $o- $+o #!$#7+/4 # (3. /o ).

    • TYPE B : I/ 1 6o 6$+ 7+/4 # o" / #2 $# /o 4 $o$+o #!$# +$!"$ / (0. ).

    • TYPE C: I/ /< $ 1 8 12 o 1"# $+o #!$# +$!"$ //$ "1 #/$+ 1 # 9 1 5 o42 # 5 / $ 51+/# $+o #!$#+$!"$ / 1+ 2o $2/$5 /o / #2 $# o 1"# < 9 o 2 1 9<# + o / 7+/4 # #/ o $# / #2 $# 91 4 2#/1o ( * ).

    • TYPE D : I/ 1 6o 6$+ 7+/4 # o" / #2 $# /o 9o/ 4 $# 5 o8$ $+o #!$# +$!"$ /+ (0. /o * ).

    • TYPE E : I/ $ $ + /o H /< $ TEF 8 12 # $ #61 !o/ $ 81+$ o "# / #2 $# # 5 o$+o #!4+ / #/ # $

    2o $2/$5 9< # 7+/4 # ('.'- )

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    TYPES

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    INCIDENCE EPIDEMIOLOGY

    • O224 + 1 :3000 /o :' 00 16$ 91 / +. E 4#!$ 5$ 1 215$ 2$ EA #++o21#/$5 81/ $"#/4 1/

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    PATHOPHYSIOLOGY• U $ # / o $+o #!4+ 1+ 5$6$ o $5 o"

    $/ o # < !$# +$!"$ / # 5 / $ o8$ # /o" $!#+/ 12 +$!"$ / o / $ 7 +/ # / o1"1/16$ !4/. A/ '- 8$$ + o !$+/#/1o / $# < !o-/ #2 $# ! oo6$ 1+ o "$5. T8oo !1/451 # 4 o8+ 5$6$ o # 5 +$ # #/$ / $$+ 1 #/o < $"o 514" o" $+o #!4+.D$61#/1o o # /$ $5 2$ 4 # ! o8/ o / $+$ /4" $+4 /+ 1 o "#/1o o 7+/4 # 9$/8$$$+o #!4+ # 5 / #2 $#. S422$++16$ +/#!$+ 1/ $ 5$6$ o "$ / o / $ / #2 $o$+o #!$#+$ /4" 54 1 ! $"9

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    Causes

    • Co !$ 1/# TEF 2# # 1+$ 54$ /o#1 $5 4+1o o / $/ #2 $o$+o #!$# 15!$+ 54 1 ! / $/ 1 5 8$$ o $"9

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    Environmental(Acquired) Causes

    • A / o4! $ o+4 $ /o 2$ /#1 "$512#/1o +# 5 1 $2/1o + 54 1 ! $! # 2< #6$ 9$$o o+$5 #+ o++19 $ 1+ #2/o + o

    5$6$ o "$ / o $+o #!$##/ $+1#;/ #2 $o$+o #!$# 7+/4 # (EA;TEF),o $ /$ # #2/o #+ 9$$ 2o +1+/$ / <1 $5 /o / $ 5$6$ o "$ / o EA;TEF

    E o+4 $ /o "$/ 1"# o $ 54 1 !$! # 2< .• M#/$ # 51#9$/$+ "$ 1/4+ .

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    Heritable Causes

    • C o"o+o"$ # o"# 1$+ #6$ 9$$$ o /$5 1 # o 1"#/$ < * - 0 o1 516154# + 81/ EA;TEF . EA;TEF 1+ o4 5

    1 / $ o o81 ! # $4 o15< +< 5 o"$+ :• T1+o"< % ( 0. - .0 o #K$2/$5

    1 516154# +)• T1+o"< ( % o #K$2/$5

    1 516154# +)• T1+o"< 3• (Mo+#12) / 1+o"<

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    S1! + # 5 S

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    D1#! o+1+EA;TEF "#< 9$ +4+ $2/$5 prenatally 1 • ultrasound examination $6$# + o <

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    Treatment o&Mani&estations

    • I 1/1# o+/ #/# 1 /$ 6$ /1o , #1"$5 #/

    "1 1"1 1 ! / $ 1+ o #+ 1 #/1o $4"o 1#,/< 12# < 1 2 45$+ / $ $ 1"1 #/1o o o #$$5+, #2$"$ / o # +42/1o 2#/ $/$ /o# o8 2o /1 4o4+ 5 #1 #!$ o +$2 $/1o +, # 5

    $ $6#/1o o / $ $#5 o / $ 9$5 /o "1 1"1 $$ 4 .

    • I / #6$ o4+ (IV) ! 42o+$ # 5 415+ + o4 5 9$o615$5 +4 $"$ /# o

    #5"1 1+/$ $5 #+ $$5$5.• $ 1 /49#/1o 2# o/ 9$ #6o15$5, #

    o++19 $ 2o" 12#/1o 1+ / $ 2o $2/1o o #11 / $ +/o"#2 , 8 12 1 +$6$ $ 2#+$+ 2#o < 9$ $"o6$5 9< !#+/ o+/o"<

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    Treatment o&Mani&estations

    • S4 !12# $ #1 2o +1+/+ o 2 o+4 $ o / $ TEF # 5# #+/o"o+1+ o / $ $+o #!$# +$!"$ /+ .

    • S4 !12# $ #1 "#< $$5 /o 9$ 5$ #

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    Treatment o&Mani&estations

    S4 !$

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    NURSING MANAGEMENT.@A++$++ o +

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    NURSING MANAGEMENT @ A5"1 1+/$ IV 415+ /o $6$ / 5$

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    CLIENT TEACHING FOR SELF-CARE

    @ I 6o 6$ # $ /+ 1 2# $ o 1 # / /o #21 1/#/$9o 51 ! 9< "$# + o /o42 # 5 $

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    COMPLICATIONS• T#2 $o"# #21# (8$# $++ o

    / #2 $# 8# ) A #+/o"o/12 $#(/$ +1o ) S/ 12/4 $+ ( # o81 !,$+o #!$# 51 #/1o ) D

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    $ $ $ 2$• www.cincinnatichildrens.org/health/info/ent/diagnose/t

    rach- stular.htm• Boxwell, G. (Ed), (2000). eonatal intensi!e care

    nursing. "ondon# $outledge% &ha'ter , *urgical +s'ects% '' - 2

    • &ham ers +, 1 ones, *. (eds).200 . *urgicalnursing of children, Edin urgh# Butterworth3einemann Else!ier, &ha'ter 4, eonatal ursing.

    • Ghai 56, 6aul 7 6aul, Bagga +r!ind. Essential6ediatrics . &B* 'u lishers. th edition. 6'

    ehar an singh . &are of new orn. 8 th edition. *agar 'u lications. 6' 9 aril:n . 3oc;en err: ,