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RHEUMATOLOGY SECTION INTERNAL MEDICNE BOARD REVIEW COURSE
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RHEUMATOLOGY SECTION INTERNAL MEDICNE BOARD REVIEW COURSE.

Dec 31, 2015

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Cameron Golden
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Page 1: RHEUMATOLOGY SECTION INTERNAL MEDICNE BOARD REVIEW COURSE.

RHEUMATOLOGY SECTIONINTERNAL MEDICNE

BOARD REVIEW COURSE

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ANATOMY REVIEW

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SERONEGATIVE SPONDYLOARTHROPATHIES

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SNSA’s

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SNSA UNIFYING FEATURES• sacroiliac joint involvement (axial disease) with inflammatory back pain• peripheral joint involvement (non-axial disease)• no RF• extra-articular features:

• HLA-B27• enthesopathy• dactylitis• mucocutaneous disease• conjunctivitis/uveitis• cardiac disease (valvular / conduction)

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SNSA’s

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SNSA’s

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SNSA’s

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SNSA’s

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HLA-B27

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HLA-B27

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ANKYLOSING SPONDYLITIS

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AS / PULMONARY DISEASE

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AS / CARDIAC DISEASE

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SACROILIITIS

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SACROILIITIS

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SPONDYLITIS

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REITER’S / REACTIVE ARTHRITIS

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PSORIATIC ARTHRITIS

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PSORIATIC ARTHRITIS

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PSORIATIC ARTHRITIS

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IBD-Related Arthritis

• Peripheral (parallels IBD activity)

• Axial (does not parellel, more HLA B27+)

• Other extraintestinal features– Uveitis– Sclerosing Cholangitis– E. nodosum– Pyoderma gangrenosum

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RHEUMATOID ARTHRITIS

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RA - PANNUS

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RA

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RA & C-SPINE

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RA & C-SPINE

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RA & C-SPINE

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FELTY’S SYNDROME

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FS & LGL

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RAEXTRAARTICULAR

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RA - EYE

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RA - PULMONARY

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RA & RHEUMATOID NODULE

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INFECTIOUS ARTHRITIS

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DISSEMINATED GC

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NONGONOCOCCAL BACTERIAL ARTHRITIS

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NONGONOCOCCAL ARTHRITIS

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INFECTIOUS BURSITIS

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TUBERCULOUS ARTHRITIS

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POTT’S DISEASE

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PARVOVIRUS

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LYME

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LYME - ECM

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ACUTE RHEUMATIC FEVER

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ACUTE RHEUMATIC FEVER

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ACUTE RHEUMATIC FEVERE. MARGINATUM

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CRYSTALLINE ARTHRITIS

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CRYSTALLINE ARTHRITIS

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GOUT

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GOUT

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GOUT

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GOUT

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CRYSTALLINE ARTHRITIS

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CPPD

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HADDHYDROXYAPATITE DEPOSITION

DISEASE

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CALCIUM OXALATE

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FIBROMYALGIA

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FIBROMYALGIA

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HIV-ASSOCIATED ARTHROPATHIES

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HIV

• Incomplete Reiter’s

• PsA

• RA goes away..

• Myopathies

• “DILS”

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OSTEOARTHRITIS

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OSTEOARTHRITIS

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NODAL OSTEOARTHRITIS

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OSTEOARTHRITISHIP

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EROSIVE OA

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OSTEOARTHRITISDISH

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OSTEOARTHRITISOCHRONOSIS

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OSTEOARTHRITISHEMOCHROMATOSIS

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OSTEOARTHRITISNEUROPATHIC

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OSTEOARTHRITISAVN

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OSTEOARTHRITISAVN

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AMYLOIDOSIS

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AMYLOIDOSIS

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AMYLOIDOSISPRIMARY

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AMYLOIDOSISABDOMINAL / RECTAL BX

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SARCOIDOSIS

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SARCOIDOSIS

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REFLEX SYMPATHETIC DYSTROPHY

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REFLEX SYMPATHETIC DYSTROPHY

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REFLEX SYMPATHETIC DYSTROPHY

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OFFICE ORTHOPEDICS

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OFFICE ORTHOPEDICS

1. Shoulder

2. Elbow

3. Hip

4. Knee

5. Back

6. Hand

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ENDOCRINE ASSOCIATED ARTHROPATHIES

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HYPERPARATHYROIDISM

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HEMOCHROMATOSIS

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DIABETIC ARTHROPATHY

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TUMOR ASSOCIATED ARTHROPATHIES

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TUMOR ASSOCIATED ARTHROPATHEIS

• DM / PM• HPO• Palmar fasciitis• Raynaud’s• Vasculitis• MDS• PMR• Sweet’s• Erythromelalgia

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SLE

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SLE

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SLE

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SLE

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SLE

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SLE

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SLE

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SLE

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SLE

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SLE

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Drug-Induced SLE

• Clinically the same except no renal or kidney disease

• Anti-histone antibody• No anti-Smith or anti-ds dna aby• Complements normal• Drugs: INH, procainamide, hydralazine• Treatment. Short course of NSAIDs or

steroids and DC offending drug

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SLE

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LIVEDO RETICULARIS

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SLE

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SLE

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SLE

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NEONATAL CUTANEOUS LUPUS

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MCTD

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Sjogren’s Syndrome

• Sicca complex– Keratoconjunctivitis (lacrimal gland)– Oral sicca (parotid)– Lymphocytic infiltrate (CD4)– SSA (Ro), SSB (La), RF, ANA, polyclonal

gammopathy– Woman age 30-50– Extraglandular

• ILD, PBC, vasculitis, neuropathy, arthritis, Raynaud’s, fever, fatigue, adenopathy/lymphoma, Hashimoto’s, myositis

– Primary vs secondary (RA)

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VASCULITIS

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Cholesterol Emboli Syndrome

-blue toes after an intervention- TIA- ARF- microhematuria- fever- ischemic bowel- eosinophilia- ESR increased- heparinization may worsen by releasing clefts from plaques

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HYPERSENSITIVITY VASCULITIS / HSP

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CRYOGLOBULINEMIA

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CRYOGLOBULINEMIA

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CRYOGLOBULINEMIA

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BEHCET’S

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BEHCET’S

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ANCAC-ANCA (PR3)-Wegener’sP-ANCA (MPO)-CSS/MPA

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WEGENER’S

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POLYARTERITIS NODOSA

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POLYARTERITIS NODOSA

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POLYARTERITIS NODOSA

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KAWASAKI

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KAWASAKI

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GIANT CELL ARTERITIS

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PMR

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PMR

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GIANT CELLARTERITIS

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TAKAYASU’S

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SCLERODERMA

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MORPHEA & LINEAR SCLERODERMA

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CREST

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PSS SKIN

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SCLERODERMA GI

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SCLERODERMA GI

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SCLERODERMA ANTIBODIES

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SCLERODERMA LUNG

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SCLERODERMA KIDNEY

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EOSINOPHILIC FASCIITIS

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POLYMYOSITIS / DERMATOMYOSITIS

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PM /DM

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DM

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GOTTRON’S (DM)

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IBM

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PM /DM

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DM

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