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Physically Disabling Conditions Part II Part II
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Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Dec 25, 2015

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Hope Douglas
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Page 1: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Physically Disabling Conditions

Part IIPart II

Page 2: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

MDMD

• Md’s = genetic, progressive muscle wasting and weakness disorders.

• Characteristics – Tire quickly– Lose fine motor control– Progressive weakness –postural changes

Page 3: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Types of MDTypes of MD

• Duchenne– X-linked– Affects pelvic girdle followed by shoulder

girdle– Most serious of MD’s

Page 4: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

SYMPTOMS

Page 5: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Becker MDBecker MD

• X-linked

• Less severe

• Imitates Duchenne – progress is slower

• Wheelchairs in 20’s

Page 6: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

AmputationsAmputations

• Acquired

• Congenital

Page 7: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• Prosthetic devices– Cost of devices– Need for new prosthetics every 18 months

• ( could you wear the same pair of shoes everyday for years on end?)

• Insurance – the haves versus the have nots• Jordan Thomas

– http://www.cnn.com/video/#/video/living/2009/08/27/cnnheroes.jordan.thomas.cnn

Page 8: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

DwarfismDwarfism

• Achondroplasia – most common type– 1 in 26,000

a)Proportionate – body parts are in proportion, but short in height

- Deficiency in pituitary gland

Page 9: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

b) Disproportionate –

- Short arms, short legs, normal torso , large head

- Faulty gene = failure of bone to fullydevelop

Page 10: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Friedreich’s AtaxiaFriedreich’s Ataxia

• Neurological disorder

• Damages peripheral nerves, cerebellum, heart

Page 11: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Multiple SclerosisMultiple Sclerosis

Page 12: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Spinal Cord InjuriesSpinal Cord Injuries

Page 13: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Congenital & Acquired ParalysisCongenital & Acquired Paralysis

• Spina Bifida

Page 14: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Types of SBTypes of SB

• Meningomyelocele (MM)

• Meningocele – spinal cord covering out

• Occulta

• Non-progressive

• No cure

Page 15: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• Hydrocephalus

• Shunts

• Bladder-bowel control

Page 16: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• Obesity

• Skin lesions

• Role models – – Jean Driscoll– Boston Marathon winner– Spina Bifida– Champaign-Urbana

Page 17: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

AcquiredAcquired• Spinal Cord Ijuries:

• traumatic or non-traumatic– Sudden blow to spine– Arthritis, cancer, infections, disk degeneration

Page 18: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

TypesTypes

• Paraplegia

• Quadriplegia (aka) Tetraplegia

Page 19: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

FactsFacts

• Males = 80 % of SCI ( Mayo Clinic, 2006)

• Incidence

• Sex

• Age

Page 20: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

EtiologyEtiology

• Crashes = 47.5%

• Falls = 22.9%

• Violence = 13.8%

• Sports = 8.9%

Page 21: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

CostsCosts

• Paraplegic: 1st year = $ 260,000– Each subsequent year - $26,000

• Low Tetra (C5-C8) = $459,000– Each subsequent year - $52,000

• High Tetra(C1-C4) = $ 710,000– Each subsequent year = $127,000

Page 22: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• Leading cause of death – renal failure

Page 23: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

Physical EducationPhysical Education

• Brockport Physical Fitness test

• Wheelchair softball– http://www.wheelchairsoftball.org/

classification.htm– http://www.wheelchairsoftball.org/#– http://www.wheelchairsoftball.org/rules.htm

Page 24: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• Wheelchair basketball

• Wheelchair rugby

Page 25: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• http://www.nlm.nih.gov/medlineplus/tutorials/spinalcordinjury/htm/index.htm

• http://www.disability.uiuc.edu/athletics/

• http://www.murderballmovie.com/

• http://www.unitedspinal.org/spinal-cord-disability-links/accessible-wheelchair-sports-recreation-travel/

Page 26: Physically Disabling Conditions Part II. MD Md’s = genetic, progressive muscle wasting and weakness disorders. Characteristics –Tire quickly –Lose fine.

• http://www.pvamagazines.com/sns/