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PED PATHOLOGY Peds lecture pt 2
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PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

Dec 29, 2015

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Page 1: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

PED PATHOLOGY

Peds lecture pt 2

Page 2: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

PEDIATRIC IMAGING & PATHOLOGY

Reviewed 5/2008

Page 3: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

PATH REVIEW (VOL3 pg 179)

• Congential: Club Foot & Hip Dysplasia• Fractures: Greenstick, Torus or buckle• Hirschsprung’s (Megacolon)• INTUSSUSCEPTION• Hylaine Membrane Disease• CROUP• Osgood-Schlatters Disease• Pyloric Stenosis• Slipped Epiphysis • REFLUX• R/O FOREIGN BODY

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MORE IMAGES

Page 5: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

Pyloric stenosis

• More common in males

• Projectile vomiting

• Failure to thrive

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• CONDITION?

• REFLUX

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This CXR is within normal limits; however, when a clinical suspicion of an airway foreign body is present, a standard PA and lateral CXR are

an insufficient evaluation. A lateral neck film should be obtained to

examine the upper airway for evidence of swelling or foreign body.

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FB

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An 18 month old female presented to the Emergency Department with a history of fever, noisy breathing, a harsh cough, and drooling. The fever and coughing began yesterday, but tonight the fever is higher and the cough sounds very harsh. The sound of this cough was alarming to the parents.

The epiglottis is normal in shape.

The airway is patent.

There is pre-vertebral soft tissue swelling noted.

This radiograph is consistent with a retropharygeal abscess, not croup.

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POSITIONING FAT PADS

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ABSENCE OF DIAPHRAM

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• NOTE OPEN JOINT SPACES

• DO NOT NEED ALL• PROJECTIONS AS

DONE WITH ADULTS!

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c/o stomach ache x 1 week

Tension pneumothorax

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RDS – Respiratory Distress

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Hyaline Membrane Disease

• Acute pulmonary disorder of the newborn characterized by

• Generalized atelectasis

• Ventilation-perfusion abnormalities

• Reduced lung compliance

• M:F =1.8:1 – slightly more common in males

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Hyaline Membrane Disease

• Cause • Immature surfactant

production • (usually begins at 18-20

weeks of gestational age) • CLINICAL SIGNS• Abnormal retraction of

chest wall • Cyanosis • Expiratory grunting • Increased respiratory rate

Page 24: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

Hyaline Membrane Disease

• Predispositions • Premature infants • Cesarean section • Infants of diabetic mothers • Perinatal asphyxia • Onset

– Usually less than 2-5 hours after birth – Increases in severity from 24 to 48 hours – Then, gradual improvement after 48-72 hours

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Hyaline Membrane Disease

Imaging findings • Typically, diffuse “ground-glass” opacification of both

lungs with air bronchograms and hypoaeration

• Hypoaeration from loss of lung volume (may be counteracted by respiratory therapy)

• Fine granular pattern • Prominent air bronchograms • Bilateral and symmetrical distribution • Prognosis • Spontaneous clearing within 7-10 days (mild course in

untreated survivors) • Death in 18%

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Hyaline Membrane Disease

• Infant respiratory distress syndrome

• The term respiratory distress syndrome (RDS) has come to represent the clinical expression of surfactant deficiency

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Hyaline Membrane Disease

Page 29: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

croup vs This radiograph is consistent with a retropharygeal abscess, not croup.

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INTUSSUSCEPTION

A barium enema demonstrated an intussusception at the hepatic flexure which was successfully reduced

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• BLOCKER PLACEMENT

• GRID OR NO • GRID?

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IniencephalyHistory:Newborn girl with short neck and head tilted up toward the sky. She died approximately 24 hours after birth due to multiple anomalies

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• 10 yo –• Pain no trauma

• These radiographs demonstrate a pathologic fracture through a bone cyst of the proximal humerus.

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Osgood-Schlatter disease

• is an overuse condition or injury of the knee that causes pain and swelling below the knee area over the tibia.

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Osgood-Schlatter disease

• Growth spurts can begin any time between the ages of 8-13 for girls and 10-15 for boys.

• OSD is most common in 11 to 14 y/o• OSD is more likely in teens who participate in

sports that involve running, twisting, and jumping, such as basketball, football, volleyball, soccer, tennis, figure skating, and gymnastics.

• With exercise, the muscles place increased stress on the growth plate

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Osgood-Schlatter disease

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Osgood-Schlatter disease

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FRACTURES IN CHILDREN

• GREENSTICK- • Incomplete fracture

• TORUS OR BUCKLE-• Impacted

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FRACTURES IN CHILDREN

• GREENSTICK• TORUS OR BUCKLE

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FRACTURES IN CHILDREN

• GREENSTICK- • TORUS OR BUCKLE

Page 47: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

greenstick

• Incomplete fx

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Slipped Epiphysis• The head of femur dislocates into the

epiphysis

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Slipped Epiphysis• One foot might point outward more than

the other, or one leg may be slightly longer than the other.

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Slipped Epiphysis

11 yo with a limp

Bilateral with worse on the right side

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R/O Child Abuse

• Skeletal Survey• Bone Scan

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Buckle or Corner Fx’s

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• Moderate distention of several loops of bowel

• (lg or small?? )

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• Hirschsprung's disease is a rare disorder occurring in about 1 out of every 5,000 to 10,000 newborn babies

• by way of comparison, constipation occurs in as many as 1 out of every 5 to 10 children).

• This disease is much more common in boys than girls.

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Hirschsprung’s diseasemegacolon

• Hirschsprung's disease is a blockage of the large intestine due to improper muscle movement in the bowel.

• It is a congenital condition, which means it is present from birth

Page 64: PED PATHOLOGY Peds lecture pt 2. PEDIATRIC IMAGING & PATHOLOGY Reviewed 5/2008.

• The intestine is constantly squeezed tight, preventing stool from passing.

• Almost all children with Hirschsprung's disease have problems with constipation from the day they are born; as many as half of babies with Hirschsprung's disease will not pass their first bowel movement during the first 36 hours of life

• There is currently no evidence to indicate that Hirschsprung's disease is caused by any medications or exposures to toxins during pregnancy.

• If a child has Hirschsprung's disease, some form of surgery is usually required to eliminate the problems with constipation.

Hirschsprung’s diseasemegacolon

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Hirschsprung’s diseasemegacolon

•Most of the time, when a doctor is concerned about the possibility of Hirschsprung's disease, he or she will have a barium enema performed. 

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Hirschsprung’s diseasemegacolon

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Megacolon can also occur in adults

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FETAL DEMISE +CONGENITAL ABNORMALITIES

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