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Four month-old baby with cyanosis Isabel Roca HU Vall Hebron
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Four month-old baby with cyanosis - NUCLEUS

Feb 09, 2022

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Page 1: Four month-old baby with cyanosis - NUCLEUS

Four month-old baby with cyanosis

Isabel RocaHU Vall Hebron

Page 2: Four month-old baby with cyanosis - NUCLEUS

CLINICAL STATEMENTMale child 3 mo oldAdmitted because of cyanosis and hypoxemia, unmodified after O2 therapyChest X-Ray showed an opacity in the left upper field

Contrast-enhanced cardiac US showed a Right-to-left shunt

Page 3: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

WHAT TO DO NEXT?1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

Page 4: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

WHAT TO DO NEXT?1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

Page 5: Four month-old baby with cyanosis - NUCLEUS

PERFUSION LUNG SCANPERFUSION LUNG SCAN

Cold defect at the left upper lobeHypoperfusion of the whole left lungSystemic activity: Right-to-Left shunt

QS/QP ratio = 1.28

Cold defect at the left upper lobeHypoperfusion of the whole left lungSystemic activity: Right-to-Left shunt

QS/QP ratio = 1.28

Page 6: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?1. CT scan2. Pulmonary artery angiography3. MRI4. Cardiosurgery

WHAT TO DO NEXT?1. CT scan2. Pulmonary artery angiography3. MRI4. Cardiosurgery

Page 7: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?1. CT scan2. Pulmonary artery angiography3. MRI4. Cardiosurgery

WHAT TO DO NEXT?1. CT scan2. Pulmonary artery angiography3. MRI4. Cardiosurgery

Treatment: selective embolisation

Page 8: Four month-old baby with cyanosis - NUCLEUS

FOLLOW-UP

Chest x-ray

Perfusion lung scan

• No systemicactivity

Page 9: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?

1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

WHAT TO DO NEXT?

1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

8 months laterrelapse of cyanosis and hypoxemia, unmodified after

O2 therapy

CLINICAL FOLLOW-UP

Page 10: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?

1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

WHAT TO DO NEXT?

1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

8 months laterrelapse of cyanosis and hypoxemia, unmodified after

O2 therapy

CLINICAL FOLLOW-UP

Page 11: Four month-old baby with cyanosis - NUCLEUS

WHAT TO DO NEXT?1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

WHAT TO DO NEXT?1. CT scan2. Perfusion lung scan3. MRI4. Cardiosurgery

Systemic activityRight-to-left shuntQS/QP ratio 1.25:1

Page 12: Four month-old baby with cyanosis - NUCLEUS

•Pulmonary arterovenous fistulae may be multiple, and theymay open at different ages.

•Perfusion lung scan allows a non-invasive, sensitive and reproducible quantification of right-to left-shunts, thatcorrelates with hypoxemia

TEACHING POINTS