Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease.

Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease 

Arnthor Ævarsson, Jacinta L Chuang, R Max Wynn, Stewart Turley, David T Chuang, Wim GJ Hol 

Structure Volume 8, Issue 3, Pages 277-291 (March 2000)

DOI: 10.1016/S0969-2126(00)00105-2

Figure 1

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 2

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 3

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 4

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 5

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 6

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 7

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Figure 8

Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)