Case Study On Dandy Walker Syndrome Done by : Sajeda Moh’d
Case Study On Dandy Walker
SyndromeDone by : Sajeda Moh’d
Objective
By the end of this presentation you will be able to:-
• Discuss the Child’s History, family history, and chief complain.
• Discuss the effect of disease on the growth and development of child.
• Define dandy walker syndrome
• Indentify the incidence of dandy walker syndrome.
• Identify the Etiologies and Predisposing Factors.
Objectives
By the end of this presentation you will be able to:-
• Discuss the Pathophysiology of dandy walker syndrome.
• Identify the Clinical Manifestations
• Identify the Diagnostic Tests
• List the possible Complications of dandy walker syndrome.
• Discuss the Medical, Surgical, and nursing Management.
• Discuss a nursing care plan.
• Identify Health Education
History of the Child S.Y
B/O Y
5years old, Bahraini female.
admitted on 6/1/2011
Chief complain:-
history of low grad fever, vomit for 2 weeks and
complaining of left side abdominal pain.
Background
S.Y 5 years old, known case of dandy walker syndrome with
ventriculoperitoneal shunt (VPS), admitted with abdominal pain,
vomits and fever since 2 weeks, her present weigh is 14.5. Her
vomits yellowish in color, complain of Flank pain which is at left
kidney side, and has history of painful urination which known as
dysuria.
Family history
No family history of dandy walker syndrome or any brain
problems.
• Father family: has history of Hemophilia.
• Mother is a SCT.
• Child S.Y sisters have no disease.
growth and development
• the diseases has no effect on the growth and
development of child S.Y, she live normally as her
sisters without any limitation or retardation.
Definition of dandy walker syndrome
• In children with Dandy-Walker Syndrome, the cerebellum
which is the organ that regulates movements and
coordination, either partially or completely lacks the
cerebellar vermis, which is the segment that connects the
two hemispheres, or sides, of the cerebellum
Incidence of Dandy walker syndrome
It is rare disorder that occurs in one for every 25,000 live births, mostly in females.
In Bahrain, the statistics didn’t specify the dandy walker syndrome and it shows congenital malformations, deformations and chromosomal abnormalities in general, which increase between the 1-9 ages to rich 245 cases in 2008.
Etiology and pre-disposing factors
• Unknown cause.
• family (generic) occurrence.
• gestational exposure specifically at first trimester to
infection or taking Warfarin, and alcohol.
For S.Y the cause of her disease is unknown.
Pathophysiology
during embryogenesis
cerebellar hemispheres and to the fourth ventricle changes
(unknown cause or nature)
cerebellar defect occur
results in blockage or atresia of the foramina of Magendie and Luschka
dilatation of the fourth ventricle & cysts formation which present in the back of the brain
Clinical manifestations
• Vomiting.
• Convulsions.
• Irritability.
• Lack of coordination in movements.
• Head circumference enlarged and a bulge in the back of the cranium is
present.
• Hydrocephalus.
the mean clinical manifestations for S.Y are the head circumference
enlarged and present of a bulge in the back of the cranium, and
hydrocephalus.
Diagnostic tests
Full blood count:- High WBC, indicates an inflammation and
infection. Low Red blood cells, hemoglobin, hematocrit and high red
cell size distribution indicate iron deficiency anemia and dehydration.
Manual differential: High Polymorphs, indicates infection and
inflammation.
Reticulocytes: High, in response to blood loss or treatment of iron
deficiency anemia.
Electrolytes: Normal.
Cont.. Blood c-reactive protein: High, indicates an infection or
inflammation after surgery.
Blood cross match: O+
Fasting blood sugar: Normal.
U+E+CR: Normal
Liver function test: Normal.
CT brain: present of VP shunt at same location, and bilateral basal
ganglia calcification.
Renal Ultrasound test: present of cyst around the tip of up shunt in
the left upper abdominal quadrant.
Complications
• The possible complications of dandy walker syndrome are:
• Raised intracranial pressure.
• Papilledema.
VPS hunt was applied to the S.Y, which is after birth, to
prevent the complication, farther enlargement of head, and
drain the CSF.
Medical Management
1. IV.F 1250 ml ½ NS with Dextrose 5% / 24 hrs.
2. Keep NPO.
3. Maintain I/O Chart.
4. Medications: Rocephin, Gentamicin, Flagyl, Chloral hydrate,
Perfalgan, Panadol, Phenobarbitone, and Valium
Surgical Management
o The doctors decided to apply the ventriculoperitoneal shunt (VPS)
to child S.Y after confirming the diagnosis with dandy walker
syndrome.
o Ventriculoperitoneal shunting is surgery to relieve increased pressure
inside the skull due to excess cerebrospinal fluid (CSF) on the brain.
Post operative complications
1. Infection.
2. VP shunt malfunction.
3. Increase intracranial pressure.
VP shunt placement
Nursing Management
Observe for sings of increase intracranial pressure, and if it happens
report the doctor immediately.
Administer prescribed medications to improve child condition.
Observe signs of infection and check vital signs Q4 hours.
Support the family by providing total information about their child.
.
Nursing care plan:-
• Patient problem:-
Post Ventriculoperitoneal shunt complication which is infection.
• Nursing Diagnosis:-
Infection R/T ventriculoperitoneal shunt placement
• Immediate goal:-
At the end of the shift, the child will not manifest signs and symptoms
of infection such as an elevation in body temperature, and redness.
Nursing intervention:
1. Monitor vital signs every 4 hours.
2. Maintain a Proper wound care & hygiene..
3. Make sure the dressing is clean & dry.
4. Advice the parent to give the child juices high in vitamins like
orange and lemon as she tolerate.
5. Give antibiotic such as IV Rocephin according to the Dr’s order
6. Report to Dr immediately if fever persists and wound has any signs
of infection such as redness, swelling, discharges.
Health Education
• Observe for abdominal distention.
• Provide a balance vitamins rich diet to the child.
• The signs and symptoms of shunt failure are persistent headache,
emesis, , change in the neurologic exam, and visual changes and if it
occur inform the doctor immediately.
• Instruct the child to avoid contact sports that may cause injury to the
shunt valve or head trauma. Instead, parents are advised to encourage
participation in low impact sports such as tennis or swimming.
• Observe signs and symptoms of bleeding and infection and if it
appear report immediately.