BEHÇET BEHÇET HASTALIĞI HASTALIĞI Prof.Dr. Mustafa ŞENOL Prof.Dr. Mustafa ŞENOL Emekli Öğretim Üyesi Emekli Öğretim Üyesi
Jan 21, 2016
BEHÇET BEHÇET
HASTALIĞIHASTALIĞI
Prof.Dr. Mustafa ŞENOLProf.Dr. Mustafa ŞENOL
Emekli Öğretim ÜyesiEmekli Öğretim Üyesi
Prof. Dr. Hulusi BEHÇET1889-1948
ETYOLOJİETYOLOJİ
• GENETİK FAKTÖRLERGENETİK FAKTÖRLER
• ENFEKSİYÖZ FAKTÖRLERENFEKSİYÖZ FAKTÖRLER
• İMMÜNOLOJİK FAKTÖRLERİMMÜNOLOJİK FAKTÖRLER
• ÇEVRESEL FAKTÖRLERÇEVRESEL FAKTÖRLER
Diagnostic criteria of Behçet syndrome
research committee of Japan – Major featuresMajor features
• Recurrent aphthous ulceration of the oral mucous membrane Recurrent aphthous ulceration of the oral mucous membrane • Skin lesions - Erythema nodosum–like lesions, subcutaneous thrombophlebitis, Skin lesions - Erythema nodosum–like lesions, subcutaneous thrombophlebitis,
folliculitis (acnelike lesions), cutaneous hypersensitivity folliculitis (acnelike lesions), cutaneous hypersensitivity • Eye lesions - Iridocyclitis, chorioretinitis, retinouveitis, definite history of Eye lesions - Iridocyclitis, chorioretinitis, retinouveitis, definite history of
chorioretinitis or retinouveitis chorioretinitis or retinouveitis • Genital ulcersGenital ulcers
– Minor features Minor features • Arthritis without deformity and ankylosis Arthritis without deformity and ankylosis • Gastrointestinal lesions characterized by ileocecal ulcers Gastrointestinal lesions characterized by ileocecal ulcers • Epididymitis Epididymitis • Vascular lesions Vascular lesions • Central nervous system symptomsCentral nervous system symptoms
– Diagnosis Diagnosis • Complete - Four major features Complete - Four major features • Incomplete - (1) 3 major features, (2) 2 major and 2 minor features, or (3) Incomplete - (1) 3 major features, (2) 2 major and 2 minor features, or (3)
typical ocular symptom and 1 major or 2 minor features typical ocular symptom and 1 major or 2 minor features • Possible - (1) 2 major features or (2) 1 major and 2 minor featuresPossible - (1) 2 major features or (2) 1 major and 2 minor features
MAGIC SENDROMU
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