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asopharyngealAngiofibroma
Dr. Vishal Sharma
A i fib
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Definition
Benign tumor of nasopharynx (?), locally
nvasive, extremely vascular occurs in
!olescent males.
amartomatous ni!us of vascular tissue,
epen!ent on testosterone.
ynonyms" nasopharyngeal fibroma,
angiofibroma
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Site of originArises in posterior nasal cavity, near superior
bor!er sphenopalatine
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Sphenopalatine foramen
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#athology
ross" Sessile, bi$lobe!, rubbery, re!$pin% or
ray colour.
istology" &ncapsulate!, compose! of vascular
ssue fibrous stroma. Vessels are thin$'alle!,
c% elastic fibers smooth muscle (this lea!s
uncontrolle! blee!ing).
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istopathology
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Small tumour
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asal cavity
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asal cavity #..S.
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asopharynx
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#terygopalatine fossa
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*nfratemporal fossa
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*nfratemporal fossa
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+hee%
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rbit
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Sphenoi! sinus
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-i!!le cranial fossa
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#ituitary +avernous sinus
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Sprea!
nterior" asal cavity paranasal sinus
sterior" asopharynx
ateral" goes to #terygopalatine fossa
/. *nfratemporal fossa chee%
0. *nferior orbital fissure
orbit
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Sprea!
uperior" /. Sphenoi! sinus
-i!!le cranial fossa
+avernous sinus
ptic chiasma
#ituitary fossa
0. S%ull base
-i!!le cranial fossa
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Symptoms
asal obstruction (12$324) 'ith !enasal
peech (rhinolalia clausa)
pistaxis (52$624)" #ersistent, #ainless,
#rofuse, #aroxysmal, 7nprovo%e!
ea!ache (054)
acial s'elling (024)" chee% palatal s'elling
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8acial s'elling
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Signsasal or asopharyngeal mass (124)
rog$face !eformity"
i!ge broa!ening
titis me!ia 'ith effusion"
to bloc%age
rismus" involvement of pterygoi! muscle
volvement of **, ***, *V, V* cranial nerve
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.9. scan #..S. 'ith contrast
xtent of tumor
nterior bo'ing of
osterior maxillary
all (-iller olman:s
ntral sign)
umor enhancement
one !estruction
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ther *nvestigations
.;.*." for intra$cranial involvement
igital Subtraction Angiography (D.S.A.)"
. extent of tumor
. tumour blush (!ue to increase! vascularity)
. fee!ing arteries for emboli
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agnetic ;esonance *maging
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D.S.A. before emboli
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D.S.A. after emboli
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Differential !iagnosis
;hab!omyosarcoma
Antrochoanal polyp
9eratoma
Dermoi!
&ncephalocoele
*nverting papilloma
S=uamous cell carcinoma
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Stagingtage *" 9umor limite! to nasal cavity or
nasopharynx 'ith no bony !estructiontage **" 9umor inva!ing pterygopalatine
fossa or paranasal sinuses
tage ***" 9umor inva!ing infratemporal
fossa or orbit or parasellar region
tage *V" 9umor inva!ing cavernous sinus
or optic chiasma or pituitary fossa
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#re$op re!uction oftumorvascularity
&mboli
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9rans$palatal approach
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9rans$palatal approach
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9rans$palatal approach
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Sar!ana:s approach
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&n!oscopic approach
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@ateral rhinotomy approach
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@ateral rhinotomy approach
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-i!facial !egloving
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Den%er:s incision
l!'ell @uc incision exten!e! me!ially till mi!line
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@e 8ort / osteotomy
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nfratemporal fossa approach
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nterior subcranial approach
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Surgical approaches
9rans$palatal approach (ilson)
small tumour in nasopharynx
Sublabial 9rans$palatal approach (Sar!ana)
large tumour of nose #S nasopharynx
*ntranasal en!oscopic approach
small tumour in nose #S nasopharynx
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Surgical approaches
9ransmaxillary approach via"
&xten!e! lateral rhinotomy incision
-i!facial !egloving incision
Den%er:s exten!e! +al!'ell$@uc incision
@e 8ort / osteotomy approach
Done for extension into pterygopalatine fossa
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Surgical approaches
*nfratemporal fossa approach (8isch)
extension into infratemporal fossa
Anterior subcranial approach
intracranial orbital extension
*mage$gui!e!, en!oscopic, laser$assiste!
removal (latest)" small me!ium si
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Surgical specimen
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Surgical specimen
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oton Stereotactic ;a!iation9herapy (#.S.;.9.)
onym" >amma %nife surgery
! for" . *ntracranial
0. ;ecurrence after surgery
ingle relatively high !ose of ra!iation !elivere!
recisely to a small area to %ill tumor cells
inimal inCury to a!Cacent nerves brain tissue
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Stereotactic ;a!iotherapy
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