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8-nasopharyngeal-angiofibroma1.doc

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    asopharyngealAngiofibroma

    Dr. Vishal Sharma

    A i fib

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    Definition

    Benign tumor of nasopharynx (?), locally

    nvasive, extremely vascular occurs in

    !olescent males.

    amartomatous ni!us of vascular tissue,

    epen!ent on testosterone.

    ynonyms" nasopharyngeal fibroma,

    angiofibroma

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    Site of originArises in posterior nasal cavity, near superior

    bor!er sphenopalatine

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    Sphenopalatine foramen

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    #athology

    ross" Sessile, bi$lobe!, rubbery, re!$pin% or

    ray colour.

    istology" &ncapsulate!, compose! of vascular

    ssue fibrous stroma. Vessels are thin$'alle!,

    c% elastic fibers smooth muscle (this lea!s

    uncontrolle! blee!ing).

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    istopathology

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    Small tumour

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    asal cavity

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    asal cavity #..S.

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    asopharynx

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    #terygopalatine fossa

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    *nfratemporal fossa

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    *nfratemporal fossa

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    +hee%

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    rbit

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    Sphenoi! sinus

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    -i!!le cranial fossa

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    #ituitary +avernous sinus

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    Sprea!

    nterior" asal cavity paranasal sinus

    sterior" asopharynx

    ateral" goes to #terygopalatine fossa

    /. *nfratemporal fossa chee%

    0. *nferior orbital fissure

    orbit

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    Sprea!

    uperior" /. Sphenoi! sinus

    -i!!le cranial fossa

    +avernous sinus

    ptic chiasma

    #ituitary fossa

    0. S%ull base

    -i!!le cranial fossa

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    Symptoms

    asal obstruction (12$324) 'ith !enasal

    peech (rhinolalia clausa)

    pistaxis (52$624)" #ersistent, #ainless,

    #rofuse, #aroxysmal, 7nprovo%e!

    ea!ache (054)

    acial s'elling (024)" chee% palatal s'elling

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    8acial s'elling

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    Signsasal or asopharyngeal mass (124)

    rog$face !eformity"

    i!ge broa!ening

    titis me!ia 'ith effusion"

    to bloc%age

    rismus" involvement of pterygoi! muscle

    volvement of **, ***, *V, V* cranial nerve

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    .9. scan #..S. 'ith contrast

    xtent of tumor

    nterior bo'ing of

    osterior maxillary

    all (-iller olman:s

    ntral sign)

    umor enhancement

    one !estruction

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    ther *nvestigations

    .;.*." for intra$cranial involvement

    igital Subtraction Angiography (D.S.A.)"

    . extent of tumor

    . tumour blush (!ue to increase! vascularity)

    . fee!ing arteries for emboli

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    agnetic ;esonance *maging

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    D.S.A. before emboli

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    D.S.A. after emboli

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    Differential !iagnosis

    ;hab!omyosarcoma

    Antrochoanal polyp

    9eratoma

    Dermoi!

    &ncephalocoele

    *nverting papilloma

    S=uamous cell carcinoma

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    Stagingtage *" 9umor limite! to nasal cavity or

    nasopharynx 'ith no bony !estructiontage **" 9umor inva!ing pterygopalatine

    fossa or paranasal sinuses

    tage ***" 9umor inva!ing infratemporal

    fossa or orbit or parasellar region

    tage *V" 9umor inva!ing cavernous sinus

    or optic chiasma or pituitary fossa

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    #re$op re!uction oftumorvascularity

    &mboli

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    9rans$palatal approach

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    9rans$palatal approach

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    9rans$palatal approach

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    Sar!ana:s approach

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    &n!oscopic approach

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    @ateral rhinotomy approach

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    @ateral rhinotomy approach

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    -i!facial !egloving

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    Den%er:s incision

    l!'ell @uc incision exten!e! me!ially till mi!line

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    @e 8ort / osteotomy

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    nfratemporal fossa approach

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    nterior subcranial approach

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    Surgical approaches

    9rans$palatal approach (ilson)

    small tumour in nasopharynx

    Sublabial 9rans$palatal approach (Sar!ana)

    large tumour of nose #S nasopharynx

    *ntranasal en!oscopic approach

    small tumour in nose #S nasopharynx

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    Surgical approaches

    9ransmaxillary approach via"

    &xten!e! lateral rhinotomy incision

    -i!facial !egloving incision

    Den%er:s exten!e! +al!'ell$@uc incision

    @e 8ort / osteotomy approach

    Done for extension into pterygopalatine fossa

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    Surgical approaches

    *nfratemporal fossa approach (8isch)

    extension into infratemporal fossa

    Anterior subcranial approach

    intracranial orbital extension

    *mage$gui!e!, en!oscopic, laser$assiste!

    removal (latest)" small me!ium si

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    Surgical specimen

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    Surgical specimen

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    oton Stereotactic ;a!iation9herapy (#.S.;.9.)

    onym" >amma %nife surgery

    ! for" . *ntracranial

    0. ;ecurrence after surgery

    ingle relatively high !ose of ra!iation !elivere!

    recisely to a small area to %ill tumor cells

    inimal inCury to a!Cacent nerves brain tissue

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    Stereotactic ;a!iotherapy

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    9han% ou