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23 10 21 17 20 A. 17 17 20 21 20 B. 10 21 19 20 20 ICD.10 5 159
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0Û o 1 - shouman.jp

Nov 24, 2021

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Page 1: 0Û o 1 - shouman.jp

155

23

10 2117

20

A.17

17 20

21

20

B.10 21

1920

20

ICD.10

5

– 159 –

Page 2: 0Û o 1 - shouman.jp

156

1) :Chediak

2):

IgAIgG IgM

3) :X SCID ADA

4):

WASDiGeorge IgE HIES

Ataxia telangiectasia AT5) :

C.1)

1013

400 45017 400

1 114

161 2

17

1 314

1 417

2)

172 1

17

17

16 IgA

IgE172 2 DiGeorge

17

2 316 8 9

172 4

13

– 160 –

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157

172 5

3) 2019

20

52 3057.7%

3 13 2

1 IgA

6

23

1

4)3 3,4

3 3

3 4

D.

17

1)

2)17

3)

4)

175)

IgA14

21

17

21

IgE

X

– 161 –

Page 4: 0Û o 1 - shouman.jp

158

ADA

20

57.7%

2

2

2

17

E.

F.

– 162 –

Page 5: 0Û o 1 - shouman.jp

159

– 163 –

Page 6: 0Û o 1 - shouman.jp

160

1 1 1 4

– 164 –

Page 7: 0Û o 1 - shouman.jp

161

2 1 2 5

– 165 –

Page 8: 0Û o 1 - shouman.jp

162

– 166 –

Page 9: 0Û o 1 - shouman.jp

163

3 1 3 4 H20

57.7%; 30 /52

– 167 –